Popliteal pterygium syndrome: implications for orthopaedic management

Popliteal pterygium syndrome (PPS) is a rare genetic disorder that represents the association of a popliteal web with a combination of craniofacial, genitourinary, and extremity malformations. The management of fixed flexion deformity of the knee resulting from popliteal webbing, is of prime interes...

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Bibliographic Details
Published inJournal of pediatric orthopaedics. B Vol. 13; no. 3; p. 197
Main Authors Parikh, Shital N, Crawford, Alvin H, Do, Twee T, Roy, Dennis R
Format Journal Article
LanguageEnglish
Published United States 01.05.2004
Subjects
Child
Child, Preschool
Choanal Atresia - complications
Choanal Atresia - surgery
Female
Genitalia - abnormalities
Humans
Infant
Knee - abnormalities
Knee - surgery
Male
Syndrome
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Summary:Popliteal pterygium syndrome (PPS) is a rare genetic disorder that represents the association of a popliteal web with a combination of craniofacial, genitourinary, and extremity malformations. The management of fixed flexion deformity of the knee resulting from popliteal webbing, is of prime interest to the orthopaedist. The degree of popliteal webbing varies greatly. Due to this variable expression, various modalities to treat popliteal webbing exist. The presence of a short sciatic nerve in the free edge of a popliteal pterygium, is a limiting factor in surgical correction of this deformity. The popliteal web is typically the most difficult orthopaedic problem. The purpose of this report is to discuss the orthopaedic management of popliteal pterygium in eight patients.
ISSN:1060-152X
DOI:10.1097/00009957-200405000-00010