Early Detection of Pulmonary Lymphangioleiomyomatosis by Spontaneous Pneumothorax A Case Report

A 31-year-old female was admitted because of dyspnea. A chest X-ray showed pneumothorax. A computed tomography (CT) scan of the chest revealed scattered thin-walled cystic lesions in both lung fields. Pulmonary lymphangioleiomyomatosis (LAM) was confirmed by a thoracoscopic lung biopsy, which reveal...

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Bibliographic Details
Published inKita Kantō igaku (The Kitakanto Medical Journal) Vol. 53; no. 3; pp. 303 - 307
Main Authors Iwasaki, Yasuki, Tomizawa, Hiroko, Mita, Yoshinori, Mori, Masatomo, Dobashi, Kunio
Format Journal Article
LanguageEnglish
Japanese
Published The Kitakanto Medical Society 2003
Subjects
early detection
lymphangioleiomyomatosis
spontaneous pneumothorax
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ISSN1343-2826
1881-1191
DOI10.2974/kmj.53.303

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Summary:A 31-year-old female was admitted because of dyspnea. A chest X-ray showed pneumothorax. A computed tomography (CT) scan of the chest revealed scattered thin-walled cystic lesions in both lung fields. Pulmonary lymphangioleiomyomatosis (LAM) was confirmed by a thoracoscopic lung biopsy, which revealed the nodular proliferation of immature smooth muscle cells that stained positive for HMB-45, desmin, α-smooth muscle actin, progesterone receptor and estrogen receptor when examined using immunostaining techniques. Medroxyprogesterone was prescribed. This report describes the early detection of LAM using chest CT scans and a thoracoscopic lung biopsy in a patient that experienced a spontaneous pneumothorax.
ISSN:1343-2826
1881-1191
DOI:10.2974/kmj.53.303