Primary Pleomorphic Omental Rhabdomyosarcoma in an Adult: A Report of a Unique Case

Rhabdomyosarcoma (RMS) is a very rare, highly malignant neoplasm thought to originate from the pluripotent mesenchymal tissue. Predominantly diagnosed among children and teenagers, however they can also be encountered in adults. There are a few risk factors associated with RMS like family history of...

Full description

Saved in:
Bibliographic Details
Published inCurēus (Palo Alto, CA) Vol. 14; no. 1; p. e21576
Main Authors Alteerah, Ilham A, Azzuz, Raouf H, Moftah, Mohamed A, Hasen, Yousef M, Eldruki, Soad I
Format Journal Article
LanguageEnglish
Published United States Cureus 24.01.2022
Subjects
General Surgery
Oncology
Pathology
radiotherapy
primary rhabdomyosarcoma
omentum
chemotherapy
pleomorphic rhabdomyosarcoma
Online AccessGet full text

Cover

More Information
Summary:Rhabdomyosarcoma (RMS) is a very rare, highly malignant neoplasm thought to originate from the pluripotent mesenchymal tissue. Predominantly diagnosed among children and teenagers, however they can also be encountered in adults. There are a few risk factors associated with RMS like family history of malignancy and genetic syndromes like neurofibromatosis type 1, Li-Fraumeni syndrome, Noonan syndrome and Beckwith-Wiedemann syndrome; however, most cases of RMS are sporadic. Other factors like radiotherapy for other malignancy and pre-natal radiation exposure also are associated with increased risk of developing RMS. The most common reported sites for RMS are head, neck, trunk, pelvis and lower limbs. Omental involvement of primary RMS has been rarely reported in the literature. Principally, the survival of treated RMS cases has improved, primarily due to multidisciplinary management approaches. In this paper, we report a case of primary pleomorphic RMS in a 50-year-old female who presented with abdominal pain.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.21576