A pilot clinical trial of oral sodium 4-phenylbutyrate (buphenyl) in ΔF508-homozygous cystic fibrosis patients: Partial restoration of nasal epithelial CFTR function

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Bibliographic Details
Published inAmerican journal of respiratory and critical care medicine Vol. 157; no. 2; pp. 484 - 490
Main Authors RUBENSTEIN, R. C, ZEITLIN, P. L
Format Journal Article
LanguageEnglish
Published New York, NY American Lung Association 01.02.1998
Subjects
Biological and medical sciences
Medical sciences
Pharmacology. Drug treatments
Respiratory system
Human
Respiratory disease
Oral administration
Metabolic diseases
Cystic fibrosis
Genetic disease
In vivo
Chemotherapy
Randomization
Treatment
Nose
Plasma membrane
Double blind study
Digestive diseases
Adult
Epithelial cell
Mechanism of action
Pharmacokinetics
Cystic fibrosis transmembrane conductance regulator
Pancreatic disease
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ISSN:1073-449X
1535-4970
DOI:10.1164/ajrccm.157.2.9706088