Unguarded Tricuspid Valve and Pulmonary Atresia With Intact Ventricular Septum Complicated With Right Coronary Artery Fistula and Advanced Atrioventricular Block in a Fetus: A Case Report

The unguarded tricuspid valve is a rare and severe condition. When found in the fetus, they mostly undergo abortion or intrauterine death. The details of the fetal course in such cases are poorly understood. Here, we report a case of an unguarded tricuspid valve detected at 20 weeks of gestation who...

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Published inCurēus (Palo Alto, CA) Vol. 16; no. 2; p. e54209
Main Authors Oka, Hideharu, Taketazu, Mio, Imanishi, Rina, Shimada, Sorachi, Sugiyama, Saori, Nakanishi, Kentaro, Yoshizawa, Akiko, Kanai, Asako, Yokohama, Yuko, Nawa, Tomohiro, Sawada, Madoka, Takamuro, Motoki, Nakau, Kouichi
Format Journal Article
LanguageEnglish
Published United States Cureus Inc 14.02.2024
Subjects
Cardiac arrhythmia
Cardiology
Case reports
Cesarean section
Coronary vessels
Disease
Edema
Fetuses
Fistula
Gynecology
Heart rate
Obstetrics
Pediatrics
Pulmonary arteries
Ultrasonic imaging
Veins & arteries
unguarded tricuspid valve
coronary fistula
uhl’s disease
atrioventricular block
pulmonary atresia with intact ventricular septum
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Summary:The unguarded tricuspid valve is a rare and severe condition. When found in the fetus, they mostly undergo abortion or intrauterine death. The details of the fetal course in such cases are poorly understood. Here, we report a case of an unguarded tricuspid valve detected at 20 weeks of gestation who developed a complete atrioventricular block and survived in utero. The fetus also had pulmonary atresia with intact ventricular septum, Uhl's disease, hypoplastic right ventricle, noncompacted left ventricle, valvular aortic stenosis, and right coronary artery fistula to the right ventricle. Despite this serious condition, the fetal hydrops did not develop. The baby was born at 33 weeks of gestation but died on day two. Our experience suggests that some babies may survive the fetal period even with the severe type of an unguarded tricuspid valve. Hence, efficient fetal and neonatal treatment strategies for fetal unguarded tricuspid valves are crucial.
ISSN:2168-8184
2168-8184
DOI:10.7759/cureus.54209