Amyloidosis in Behcet′s disease

Behcet′s disease (BD) is a multisystem vasculitis with protean manifestations. It is characterized by a heightened state of inflammation, although the factors that initiate and sustain this inflammation are not clear. We report some cases of BD-associated amyloidosis and have similar features. The p...

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Bibliographic Details
Published inSaudi journal of kidney diseases and transplantation Vol. 26; no. 1; pp. 132 - 134
Main Authors Ghorbel, IBen, Feki, NBel, Salem, TBen, Lamloum, M, Houman, MH
Format Journal Article
LanguageEnglish
Published Wolters Kluwer Medknow Publications 2015
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Summary:Behcet′s disease (BD) is a multisystem vasculitis with protean manifestations. It is characterized by a heightened state of inflammation, although the factors that initiate and sustain this inflammation are not clear. We report some cases of BD-associated amyloidosis and have similar features. The patients developed nephrotic syndrome due to secondary amyloidosis, which was refractory to the immunosuppressive agents. Two patients expired and the third was lost to follow-up during the course. The BD complicated with amyloidosis is associated with high mortality despite the current aggressive therapy.
ISSN:1319-2442
DOI:10.4103/1319-2442.148761