Primary primitive neuroectodermal tumor of the lumbar extradural space

Primary spinal primitive neuroectodermal tumors (PNETs) of the extradural space are very rare; only 10 cases have been reported in the English language literature. The histopathological diagnosis of primary spinal PNETs has been discussed for many years. These tumors have a rapidly progressive cours...

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Bibliographic Details
Published inJournal of neurosurgery. Pediatrics Vol. 2; no. 3; p. 215
Main Authors Ozdemir, Nail, Usta, Gungor, Minoglu, Mustafa, Erbay, Ayse Mecit, Bezircioglu, Hamdi, Tunakan, Mine
Format Journal Article
LanguageEnglish
Published United States 01.09.2008
Subjects
Adolescent
Decompression, Surgical
Disease Progression
Fatal Outcome
Female
Humans
Immunohistochemistry
Lumbosacral Region
Neuroectodermal Tumors, Primitive, Peripheral - metabolism
Neuroectodermal Tumors, Primitive, Peripheral - pathology
Neuroectodermal Tumors, Primitive, Peripheral - surgery
Reoperation
Spinal Neoplasms - metabolism
Spinal Neoplasms - pathology
Spinal Neoplasms - surgery
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Summary:Primary spinal primitive neuroectodermal tumors (PNETs) of the extradural space are very rare; only 10 cases have been reported in the English language literature. The histopathological diagnosis of primary spinal PNETs has been discussed for many years. These tumors have a rapidly progressive course, and there is no current consensus on the optimal therapeutic approach for these patients. The authors present a case of primary PNET located in the lumbar extradural space in a 13-year-old girl and report the clinical, radiological, histopathological, and surgical findings. They compare their findings with those from the other 10 cases reported in the literature and review relevant literature.
ISSN:1933-0707
DOI:10.3171/PED/2008/2/9/215