Isolated Cor Triatriatum Sinister: A Case Report

• Published in: Latvijas k̦̦irurg̓ijas žurnāls Vol. 18; no. 1; pp. 28 - 30
• Main Authors: Grīnberga, Zanda, Sīlis, Pauls, Ligere, Elīna, Lubaua, Ingūna, Bergmane, Inta, Auziņa, Luīze, Šmits, Lauris, Ozoliņš, Valts, Sikora, Normunds, Lāce, Inga
• Format: Journal Article
• Language: English
• Published: Riga Sciendo 18.11.2020; De Gruyter Poland
• Subjects: Cardiovascular disease; Case reports; Children & youth; Congenital diseases; Coronary vessels; Heart; Heart defects, congenital heart disease; Laboratories; Pediatrics; Surgery; surgical repair, transthoracic echocardiography; Veins & arteries
• ISSN: 1407-981X; 2199-5737; 1407-981X
• DOI: 10.2478/chilat-2020-0007

is a rare congenital cardiac anomaly that has been identified in 0.1% of children with congenital heart disease. It is defined as a fibromuscular membrane that divides the left atrium into two chambers: a superior ( ) that in most cases receives drainage from the pulmonary veins and an inferior ( ) chamber that communicates with the mitral valve and the left atrium. can be an isolated lesion (approximately 25% of cases), but in many cases it is associated with other congenital cardiovascular anomalies, the most common one being – atrial septal defect(3). Symptoms in patients with are related to obstruction of pulmonary venous drainage, pressure loading of the right side of the heart and congestive cardiac failure. Depending on the severity of the obstruction and presence of associated cardiac anomalies it can be diagnosed at any age. Diagnosis is usually achieved by echocardiography in early infancy. Elective treatment method is surgical excision of the membrane. Here we present a pediatric patient (4 months old) presenting in cardiogenic shock with a successful correction of isolated To confirm diagnosis and success of surgical repair, transthoracic and transesophageal echocardiography were used.