Real-Life Experience with CFTR Modulators Shows Correction of LAD-IV Phenotype in Cystic Fibrosis

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Bibliographic Details
Published inAmerican journal of respiratory cell and molecular biology Vol. 71; no. 4; pp. 495 - 498
Main Authors Montresor, Alessio, D'Ulivo, Beatrice, Preato, Sara, Farinazzo, Alessia, Pintani, Emily, Chiara, Elena Dalla, Torroni, Lorena, Verlato, Giuseppe, Boscia, Silvia, Pisano, Laura, Mangone, Giusi, Ricci, Silvia, Azzari, Chiara, Taccetti, Giovanni, Terlizzi, Vito, Cipolli, Marco, Melotti, Paola, Sorio, Claudio, Laudanna, Carlo
Format Journal Article
LanguageEnglish
Published United States American Thoracic Society 01.10.2024
Subjects
Adolescent
Adult
Aminophenols - pharmacology
Aminophenols - therapeutic use
Benzodioxoles - pharmacology
Benzodioxoles - therapeutic use
Child
Child, Preschool
Cystic fibrosis
Cystic Fibrosis - drug therapy
Cystic Fibrosis - genetics
Cystic Fibrosis Transmembrane Conductance Regulator - genetics
Cystic Fibrosis Transmembrane Conductance Regulator - metabolism
Female
Humans
Male
Mutation
Phenotype
Phenotypes
Quinolines - pharmacology
Quinolines - therapeutic use
Quinolones - pharmacology
Quinolones - therapeutic use
Young Adult
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Bibliography:content type line 23
SourceType-Scholarly Journals-1
ObjectType-Correspondence-1
ISSN:1044-1549
1535-4989
1535-4989
DOI:10.1165/rcmb.2024-0136LE