Chilblain lupus with nail involvement: a case report

Chilblain lupus is a rarely manifested variant of chronic lupus. Its appearance can be sporadic or hereditary associated with an autosomal dominant mutation. The diagnosis is clinical and histopathological. The case is presented of a patient with systemic lupus erythematosus presenting with chilblai...

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Published inRevista Colombiana de Reumatología (English Edition) Vol. 29; no. 3; pp. 231 - 236
Main Authors Tamayo Buendía, María Margarita, Ordóñez-Parra, Juliana, Moreo-Mercado, Sebastián, Mejía Cortés, Maddy
Format Journal Article
LanguageEnglish
Published Elsevier España, S.L.U 01.07.2022
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Summary:Chilblain lupus is a rarely manifested variant of chronic lupus. Its appearance can be sporadic or hereditary associated with an autosomal dominant mutation. The diagnosis is clinical and histopathological. The case is presented of a patient with systemic lupus erythematosus presenting with chilblain lupus and nail involvement, despite the use of antimalarials and immunomodulators. La perniosis lúpica es una variante del lupus crónico que se manifiesta con poca frecuencia, su aparición puede ser esporádica o hereditaria, asociada con una mutación autosómica dominante, en tanto que su diagnóstico es clínico e histopatológico. Se reporta el caso de una mujer con lupus eritematoso sistémico con manifestación de perniosis lúpica y compromiso ungueal, a pesar del uso de antimaláricos e inmunomoduladores.
ISSN:2444-4405
2444-4405
DOI:10.1016/j.rcreue.2022.05.003