Coronary sinus type atrial septal defect in a child with pulmonary atresia and Ebstein's anomaly

• Published in: British Heart Journal Vol. 53; no. 4; pp. 465 - 467
• Main Authors: Russell, G A, Stovin, P G
• Format: Journal Article
• Language: English
• Published: London BMJ Publishing Group Ltd and British Cardiovascular Society 01.04.1985; BMJ; BMJ Publishing Group LTD
• Subjects: Abnormalities, Multiple; Biological and medical sciences; Cardiology. Vascular system; Congenital heart diseases. Malformations of the aorta, pulmonary vessels and vena cava; Ebstein Anomaly - complications; Female; Heart; Heart Septal Defects, Atrial - complications; Humans; Infant, Newborn; Medical sciences; Pulmonary Artery - abnormalities; Human; Concomitant disease; Congenital; Autopsy; Heart disease; Atresia; Atrial septal defect; Cardiovascular disease; Child; Pulmonary valve; Ebstein anomaly of the tricuspid valve
• ISSN: 0007-0769; 1468-201X; 2053-5864
• DOI: 10.1136/hrt.53.4.465

At birth an infant was found to have an unusual series of abnormalities with a coronary sinus type atrial septal defect complicating pulmonary atresia with an intact ventricular septum and Ebstein's anomaly. The functionally important anomalies were diagnosed by echocardiography and cardiac catheterisation. The coronary sinus defect and Ebstein's anomaly were detected only at necropsy. Although only a single case, the features of this heart favour Bull's revised classification of pulmonary atresia.