Two different anesthetic managements of a patient with von Gierke's disease

Von Gierke's disease, a form of glycogen storage disturbance, is a rare metabolic disorder with important implications for anesthesiologists. It is caused by the lack of the glucose-6-phosphatase, which is necessary for the liver to convert glycogen to glucose. To avoid severe hypoglycemia, it...

Full description

Saved in:
Bibliographic Details
Published inActa anaesthesiologica Taiwanica Vol. 44; no. 1; p. 51
Main Authors Huang, I-Ren, Jean, Wei-Horng, Lu, Cheng-Wei, Wu, Chia-Chan, Lin, Tzu-Yu, Chuang, Yueh-Hsun, Sun, Wei-Zen
Format Journal Article
LanguageEnglish
Published China (Republic : 1949- ) 01.03.2006
Subjects
Adult
Anesthesia - methods
Blood Glucose - analysis
Glycogen Storage Disease Type I - metabolism
Humans
Male
Online AccessGet more information

Cover

More Information
Summary:Von Gierke's disease, a form of glycogen storage disturbance, is a rare metabolic disorder with important implications for anesthesiologists. It is caused by the lack of the glucose-6-phosphatase, which is necessary for the liver to convert glycogen to glucose. To avoid severe hypoglycemia, it is crucial to keep oral feeding at intervals 2-3 hr for maintaining a normal blood sugar level. The metabolic derangements of von Gierke's disease may result in serious complications in patients undergoing surgery and anesthesia. We report the anesthetic managements of a patient with von Gierke's disease in two operations with different encounters.
ISSN:1875-4597