Anomalous Origin of the Left Coronary Artery from the Pulmonary Artery The Role of Multislice Computed Tomography ( MSCT )
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary abnormality also known as Bland-White-Garland syndrome. The incidence of ALCAPA is about 1 in every 300,000 live births, and constitutes 0.24% and 0.46% of all congenital cardiac disease. It...
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Published in | Oman medical journal Vol. 31; no. 5; pp. 387 - 389 |
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Main Authors | , , |
Format | Journal Article |
Language | English |
Published |
Muscat - Oman
Oman Medical Specialty Board
01.09.2016
OMJ |
Subjects | |
Online Access | Get full text |
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Summary: | Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is
a rare congenital coronary abnormality also known as Bland-White-Garland syndrome.
The incidence of ALCAPA is about 1 in every 300,000 live births, and constitutes 0.24%
and 0.46% of all congenital cardiac disease. It has a high infant mortality rate reaching up
to 90% if left untreated. For many years, the diagnosis of ALCAPA was by angiography or
autopsy. However, multislice computed tomography (MSCT) is a non-invasive imaging
tool that allows accurate, non-invasive diagnosis of ALCAPA. Here we report a case
of ALCAPA in a six-month-old girl who presented with a two-week history of cough,
fever, tachypnea, and sweating during feeding. During admission, an echocardiogram was
performed that revealed ALCAPA, which was confirmed using CT. We discuss the role
of MSCT in its diagnosis. |
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Bibliography: | OMJ.jpg Oman Medical Journal, Vol. 31, No. 5, Sep 2016: 387-389 |
ISSN: | 1999-768X 2070-5204 |
DOI: | 10.5001/omj.2016.77 |