Atypical Sézary syndrome in a young subject

• Published in: Annales de dermatologie et de vénéréologie Vol. 147; no. 5; p. 355
• Main Authors: Jabran-Maanaoui, S, Chauvet, P, Gillard, M, Carpentier, B, Pascal, L, Quinchon, J-F, Modiano, P
• Format: Journal Article
• Language: French
• Published: France 01.05.2020
• Subjects: Adult; Fatal Outcome; Humans; Male; Sezary Syndrome - pathology; Sezary Syndrome - therapy; Skin Neoplasms - pathology; Skin Neoplasms - therapy; Epidermotropic cutaneous lymphomas; Bexarotene; Chemotherapy; Syndrome de Sézary; Lymphomes cutanés épidermotropes; Béxacarotène; Extracorporeal photochemotherapy; Sézary syndrome; Photochimiothérapie extracorporelle

Sézary syndrome accounts for 5% of cutaneous T-cell lymphomas, with mean age of onset of 60 years. Erythroderma associated with palmoplantar keratoderma and lymphadenopathy is the usual clinical presentation, but the disease has potentially confusing polymorphic clinical features. We report the case...