Infratentorial angioleiomyoma: case report and review of the literature

• Published in: Revista de neurologiá Vol. 62; no. 2; pp. 68 - 74
• Main Authors: Delgado-Fernandez, Juan, Penanes, Juan R, Torres, Cristina V, Gordillo-Velez, Carlos H, Manzanares-Soler, Rafael, Sola, Rafael G
• Format: Journal Article
• Language: English; Spanish
• Published: Spain 16.01.2016
• Subjects: Adult; Angiomyoma - diagnosis; Angiomyoma - surgery; Humans; Infratentorial Neoplasms - diagnosis; Infratentorial Neoplasms - surgery; Male
• ISSN: 1576-6578
• DOI: 10.33588/rn.6202.2015374

Intracranial angioleiomyomas are extremely rare lesions. Only 22 intracranial angioleiomyomas have been described in the literature and only three were infratentorial. We report a case of an infratentorial angioleiomyoma in a 43 year-old-man, who underwent a brain computer tomography because of hearing loss. The MRI showed a 1.4 cm tumor, initially described as a meningioma, with progressive enhancement after gadolinium injection, an augmented apparent diffusion coefficient and a generalized metabolite decreased in the spectroscopy. The lesion was surgically removed through a suboccipital approach with a good evolution and without postoperative complications. In the immunohistological study, the lesion was mainly composed of multiple vessels and the immunohistochemistry was positive for actin and caldesmon. Two years after surgery, no recurrence has been found in the MRI. Angioleiomyomas diagnostic may be complex, but some radiological features could help in the differential diagnostic. Angioleiomyomas are benign tumors associated with favorable outcomes after total resection, that in our case, did not show a significant bleeding risk.