Isolated left ventricular noncompaction: a review of three different presentations for a rare disease

• Published in: Connecticut medicine Vol. 77; no. 1; p. 11
• Main Authors: Amuchástegui, Marcos, Amuchastegui, Tomas, Contreras, Alejandro Ernesto, Donohue, Thomas, Ghantous, Andre
• Format: Journal Article
• Language: English
• Published: United States 01.01.2013
• Subjects: Adolescent; Adult; Defibrillators, Implantable; Echocardiography, Doppler; Humans; Isolated Noncompaction of the Ventricular Myocardium - diagnosis; Isolated Noncompaction of the Ventricular Myocardium - diagnostic imaging; Isolated Noncompaction of the Ventricular Myocardium - pathology; Isolated Noncompaction of the Ventricular Myocardium - therapy; Male; Middle Aged

Isolated left ventricular noncompaction (ILVNC) is a rare cardiomyopathy with a genetic background characterized by numerous prominent trabeculations and deep intertrabecular recesses. It occurs in the absence of any coexisting congenital lesion or hemodynamic abnormality and is rare in the adult po...