Off-Pump Coronary Artery Bypass Graft in a Patient with Congenital Factor V Deficiency and Hereditary Spherocytosis Complicated with Stage 4 Diabetic Nephropathy
A 64-year-old man with congenital factor V deficiency and hereditary spherocytosis was attending our hospital for type II diabetes and stage 4 diabetic nephropathy. Coronary angiography performed to assess chest pain revealed severe triple-vessel disease, including total occlusion of the right coron...
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Published in | Japanese Journal of Cardiovascular Surgery Vol. 46; no. 6; pp. 296 - 300 |
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Main Authors | , , , , , , , |
Format | Journal Article |
Language | Japanese |
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The Japanese Society for Cardiovascular Surgery
15.11.2017
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Abstract | A 64-year-old man with congenital factor V deficiency and hereditary spherocytosis was attending our hospital for type II diabetes and stage 4 diabetic nephropathy. Coronary angiography performed to assess chest pain revealed severe triple-vessel disease, including total occlusion of the right coronary artery. The patient required surgical coronary revascularization. In the preoperative examination, the activated partial thromboplastin time (APTT) and prothrombin time-international normalized ratio (PT-INR) were high (89.5 s and 1.95) and factor V activity was low (6% ; normal range, 70-135%). Hemodialysis was performed on the day of the operation, and 6 units of fresh frozen plasma (FFP) were administered, which reduced immediately the preoperative PT-INR to 1.33. We performed off-pump coronary artery bypass grafting (OPCAB) and perioperatively administered 6 units of FFP with 4 units of red blood cells (RBC) transfusion. The postoperative course of the patient was uneventful, and he was discharged on postoperative day 22. Here we report the case of a patient with a very rare disease of congenital factor V deficiency and hereditary spherocytosis complicated with stage 4 diabetic nephropathy who required OPCAB. |
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AbstractList | A 64-year-old man with congenital factor V deficiency and hereditary spherocytosis was attending our hospital for type II diabetes and stage 4 diabetic nephropathy. Coronary angiography performed to assess chest pain revealed severe triple-vessel disease, including total occlusion of the right coronary artery. The patient required surgical coronary revascularization. In the preoperative examination, the activated partial thromboplastin time (APTT) and prothrombin time-international normalized ratio (PT-INR) were high (89.5 s and 1.95) and factor V activity was low (6% ; normal range, 70-135%). Hemodialysis was performed on the day of the operation, and 6 units of fresh frozen plasma (FFP) were administered, which reduced immediately the preoperative PT-INR to 1.33. We performed off-pump coronary artery bypass grafting (OPCAB) and perioperatively administered 6 units of FFP with 4 units of red blood cells (RBC) transfusion. The postoperative course of the patient was uneventful, and he was discharged on postoperative day 22. Here we report the case of a patient with a very rare disease of congenital factor V deficiency and hereditary spherocytosis complicated with stage 4 diabetic nephropathy who required OPCAB. |
Author | Sakai, Mari Doi, Toshio Yoshimura, Naoki Yokoyama, Shigeki Nagura, Saori Fukahara, Kazuaki Sakata, Kimimasa Obi, Hayato |
Author_xml | – sequence: 1 fullname: Nagura, Saori organization: First Department of Surgery, University of Toyama – sequence: 2 fullname: Fukahara, Kazuaki organization: First Department of Surgery, University of Toyama – sequence: 3 fullname: Sakai, Mari organization: First Department of Surgery, University of Toyama – sequence: 4 fullname: Doi, Toshio organization: First Department of Surgery, University of Toyama – sequence: 5 fullname: Yokoyama, Shigeki organization: First Department of Surgery, University of Toyama – sequence: 6 fullname: Sakata, Kimimasa organization: First Department of Surgery, University of Toyama – sequence: 7 fullname: Obi, Hayato organization: First Department of Surgery, University of Toyama – sequence: 8 fullname: Yoshimura, Naoki organization: First Department of Surgery, University of Toyama |
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Title | Off-Pump Coronary Artery Bypass Graft in a Patient with Congenital Factor V Deficiency and Hereditary Spherocytosis Complicated with Stage 4 Diabetic Nephropathy |
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