Dental Findings and Management in a Mucopolysaccharidosis Type IIIB Patient

• Published in: Journal of dentistry for children (Chicago, Ill.) Vol. 79; no. 3; p. 176
• Main Authors: Mellara, Talitha de Siqueira, Azevedo, Danielle Torres, Faria, Gisele, Nelson Filho, Paulo, Queiroz, Alexandra Mussolino de, Brentegani, Luiz Guilherme
• Format: Journal Article
• Language: English
• Published: United States 01.09.2012
• Subjects: Child; Dental Care for Disabled; Dental Caries - diagnosis; Dental Caries - therapy; Dental Pulp Cavity - abnormalities; Dentigerous Cyst - diagnostic imaging; Follow-Up Studies; Humans; Incisor - abnormalities; Male; Mandibular Diseases - diagnostic imaging; Molar - abnormalities; Molar, Third - abnormalities; Mucopolysaccharidosis III - pathology; Radiography; Tooth Diseases - diagnosis; Tooth Diseases - therapy; Tooth Germ - abnormalities; Tooth, Deciduous - abnormalities

Mucopolysaccharidosis type IIIB (MPS IIIB) is an autosomal recessive disorder caused by deficiency of the lysosomal enzyme a-N-acetylglucosaminidase. Affected subjects present developmental delay, attention deficit disorder, uncontrollable hyperactivity, and aggressive behavior, followed by progress...