Localized neurological necrotizing vasculitides. Three cases with isolated mononeuritis multiplex

Localized vasculitic neuropathies are increasingly reported. We describe 3 cases of peripheral neuropathy with necrotizing vasculitis confined to nerves and muscles without systemic involvement. These neuropathies were severe and relapsing, in contrast to a usually benign prognosis. Our cases appear...

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Published inJournal of rheumatology Vol. 28; no. 3; p. 631
Main Authors Abgrall, S, Mouthon, L, Cohen, P, Authier, F J, Nizou, R, Ropert, A, Ghérardi, R, Guillevin, L
Format Journal Article
LanguageEnglish
Published Canada 01.03.2001
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Abstract Localized vasculitic neuropathies are increasingly reported. We describe 3 cases of peripheral neuropathy with necrotizing vasculitis confined to nerves and muscles without systemic involvement. These neuropathies were severe and relapsing, in contrast to a usually benign prognosis. Our cases appear to be isolated vasculitic neuropathies, with vasculitis strictly limited to the peripheral neuromuscular system without nonspecific clinical and/or biological systemic involvement.
AbstractList Localized vasculitic neuropathies are increasingly reported. We describe 3 cases of peripheral neuropathy with necrotizing vasculitis confined to nerves and muscles without systemic involvement. These neuropathies were severe and relapsing, in contrast to a usually benign prognosis. Our cases appear to be isolated vasculitic neuropathies, with vasculitis strictly limited to the peripheral neuromuscular system without nonspecific clinical and/or biological systemic involvement.
Author Nizou, R
Mouthon, L
Ropert, A
Guillevin, L
Authier, F J
Ghérardi, R
Abgrall, S
Cohen, P
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Snippet Localized vasculitic neuropathies are increasingly reported. We describe 3 cases of peripheral neuropathy with necrotizing vasculitis confined to nerves and...
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SubjectTerms Aged
Biopsy
Fatal Outcome
Female
Humans
Male
Middle Aged
Mononeuropathies - etiology
Mononeuropathies - pathology
Muscle, Skeletal - blood supply
Muscle, Skeletal - pathology
Necrosis
Peripheral Nerves - blood supply
Peripheral Nerves - pathology
Recurrence
Vasculitis - complications
Vasculitis - pathology
Title Localized neurological necrotizing vasculitides. Three cases with isolated mononeuritis multiplex
URI https://www.ncbi.nlm.nih.gov/pubmed/11296972
Volume 28
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