Rosai–Dorfman disease mimicking IgG4-related diseases: a single-center experience in China

• Published in: Orphanet journal of rare diseases Vol. 15; no. 1; pp. 1 - 9
• Main Authors: Wang, Li, Li, Wei, Zhang, Shangzhu, Peng, Linyi, Shen, Min, Song, Shuoning, Zhang, Wei, Cao, Xinxin, Feng, Ruie, Zhang, Wen
• Format: Journal Article
• Language: English
• Published: London BioMed Central Ltd 14.10.2020; BioMed Central; BMC
• Subjects: Autoimmune diseases; Central nervous system; Comparative analysis; Disease; Fibrosis; Glucocorticoids; Health aspects; Histiocytosis; Immunoglobulin G; Immunoglobulin G4-related disease; Immunosuppressive agents; Laboratories; Lymphatic system; Males; Medical prognosis; Medical research; Mimicry; Nervous system; Pathology; Patients; Phlebitis; Plasma; Prognosis; Rare diseases; Rosai-Dorfman disease; Serology

Rosai-Dorfman disease (RDD) and IgG4-related (IgG4-RD) disease are both rare diseases, but in some cases, RDD mimics IgG4-RD clinically and pathologically. RDD mimicking IgG4-RDs (RDD mimic IgG4-RD), referring to disease initially diagnosed as IgG4-RD but finally pathologically confirmed to be RDD,...