IgG4-related aortitis/periaortitis and periarteritis: a distinct spectrum of IgG4-related disease

• Published in: Arthritis research & therapy Vol. 22; no. 1; pp. 103 - 11
• Main Authors: Peng, Linyi, Zhang, Panpan, Li, Jieqiong, Liu, Zheng, Lu, Hui, Zhu, Liang, Wang, Xiaorong, Teng, Fei, Li, Xuemei, Guo, Huifang, Fei, Yunyun, Zhang, Wen, Zhao, Yan, Zeng, Xiaofeng, Zhang, Fengchun
• Format: Journal Article
• Language: English
• Published: England BioMed Central Ltd 04.05.2020; BioMed Central; BMC
• Subjects: Abdomen; Aged; Allergies; Aorta, Abdominal - pathology; Aortitis; Aortitis - diagnosis; Aortitis - drug therapy; Arthritis; Biopsy; Care and treatment; Coronary vessels; Female; Glucocorticoids - therapeutic use; Humans; IgG4-related disease; Immunoglobulin E; Immunoglobulin G; Immunoglobulin G4-Related Disease - diagnosis; Immunoglobulin G4-Related Disease - drug therapy; Immunosuppressive agents; Immunosuppressive Agents - therapeutic use; Kidney diseases; Laboratories; Lymphatic system; Magnetic resonance imaging; Male; Medical imaging; Medical research; Middle Aged; Pain; Patients; Periaortitis; Periarteritis; Plasma; Retroperitoneal fibrosis; Software; Ultrasonic imaging; Veins & arteries; United States > US; Retroperitoneal fibrosis; Aortitis; IgG4-related disease; Periarteritis; Periaortitis

Large vessels could be involved in immunoglobulin (Ig)-G4-related disease (IgG4-RD). This study aimed to clarify the clinical features and evaluate the treatment efficacy for IgG4-RD with aortitis/periaortitis and periarteritis (PAO/PA). This study prospectively enrolled 587 patients with IgG4-RD wi...