Recommendations for the treatment of anti-melanoma differentiation-associated gene 5-positive dermatomyositis-associated rapidly progressive interstitial lung disease

• Published in: Seminars in arthritis and rheumatism Vol. 50; no. 4; pp. 776 - 790
• Main Authors: Romero-Bueno, F., Diaz del Campo, P., Trallero-Araguás, E., Ruiz-Rodríguez, J.C., Castellvi, I., Rodriguez-Nieto, M.J., Martínez-Becerra, M.J., Sanchez-Pernaute, O., Pinal-Fernandez, I., Solanich, X., Gono, T., Gonzalez-Gay, M.A., Plana, M.N., Selva-O'Callaghan, A.
• Format: Journal Article
• Language: English
• Published: United States Elsevier Inc 01.08.2020
• Subjects: Basiliximab; Consensus; Cyclophosphamide; Cyclophosphamide - therapeutic use; Cyclosporine; Dermatomyositis; Dermatomyositis - complications; Dermatomyositis - drug therapy; Dermatomyositis - genetics; Drug Therapy, Combination; Extracorporeal membrane oxygenation; Glucocorticoid; Glucocorticoids - therapeutic use; Humans; Immunosuppressive Agents - therapeutic use; Intensive care; Interferon-Induced Helicase, IFIH1 - genetics; Intravenous immunoglobulins; Lung Diseases, Interstitial - complications; Lung Diseases, Interstitial - drug therapy; Lung transplant; Mycophenolate; Plasmapheresis; Polymixyn B hemoperfusion; Rapidly progressive interstitial lung disease; Review; Rituximab; Syndrome; systematic; Tacrolimus; Tofacitinib; Polymixyn B hemoperfusion; Intensive care; Extracorporeal membrane oxygenation; Intravenous immunoglobulins; Dermatomyositis; Rituximab; Cyclosporine; Review; systematic; Glucocorticoid; Plasmapheresis; Mycophenolate; Cyclophosphamide; Tacrolimus; Tofacitinib; Rapidly progressive interstitial lung disease; Basiliximab; Lung transplant

The study aimed to develop evidence-based recommendations for the treatment of rapidly progressive interstitial lung disease (RPILD) associated with the anti-Melanoma Differentiation-Associated Gene 5-positive dermatomyositis (DM) syndrome. The task force comprised an expert panel of specialists in...