A Clinical Classification Scheme for Tracheobronchomegaly (Mounier-Kuhn Syndrome)

• Published in: Lung Vol. 193; no. 5; pp. 815 - 822
• Main Authors: Payandeh, Jennifer, McGillivray, Barbara, McCauley, Graeme, Wilcox, Pearce, Swiston, John R., Lehman, Anna
• Format: Journal Article
• Language: English
• Published: New York Springer US 01.10.2015; Springer; Springer Nature B.V
• Subjects: Care and treatment; Classification; Clinical trials; CT imaging; Cutis Laxa - complications; Fetoscopy - adverse effects; Fibers; Humans; Infant; Intubation, Intratracheal - adverse effects; Lung diseases; Male; Medicine; Medicine & Public Health; Middle Aged; Patients; Pneumology/Respiratory System; Pulmonary Fibrosis - complications; Respiratory Tract Infections - complications; Tracheobronchomegaly - classification; Tracheobronchomegaly - etiology; United States; Acquired cutis laxa; Mounier-Kuhn syndrome; Connective tissue diseases; Generalized elastolysis; Tracheobronchomegaly

Introduction Tracheobronchomegaly (Mounier-Kuhn Syndrome) is a rare disease characterized by tracheal enlargement and associated loss of elastic fibers in the trachea and main bronchi. Materials MEDLINE, Index Medicus, and other databases were searched with pre-defined criteria to identify cases of...