Effect of nutritional intervention on nutritional status among children with disorders of amino acid and nitrogen metabolism (AANMDs): A scoping review

• Published in: Intractable & Rare Diseases Research Vol. 10; no. 4; pp. 246 - 256
• Main Authors: Lim, Jing Ying, Ali, Nazlena Mohamad, Mohamad, Maslina, Amit, Noh, Leong, Huey Yin, Rajikan, Roslee
• Format: Journal Article
• Language: English
• Published: Japan International Research and Cooperation Association for Bio & Socio-Sciences Advancement 01.11.2021
• Subjects: amino acid metabolism; inborn errors; nutrition therapy; nutritional status; Review; nutritional status; inborn errors; nutrition therapy; amino acid metabolism

Disorders of amino acid and nitrogen metabolism (AANMDs) occur due to an enzyme deficiency in a normal biochemical pathway. Nutritional intervention is recognized as the mainstay of treatment for children diagnosed with AANMD. Hence, this scoping review aimed to identify the nutritional intervention...