The PAH patient's perspective
Pulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension asso...
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| Published in | International journal of cardiology congenital heart disease Vol. 21; p. 100596 |
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| Main Authors | , , , |
| Format | Journal Article |
| Language | English |
| Published |
Netherlands
Elsevier B.V
01.09.2025
Elsevier |
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| Online Access | Get full text |
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| Abstract | Pulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension associated with Congenital Heart Disease (PAH-CHD) face a number of different issues directly related to their condition, which range from physical limitations and uncertainty over their diagnosis, which in some cases cause significant depression and anxiety, to impact on their relationships with friends and family, financial challenges and family planning.
In this article, we interview two patients living with PAH-CHD and discuss the numerous issues that patients may face as a direct result of their condition. |
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| AbstractList | Pulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension associated with Congenital Heart Disease (PAH-CHD) face a number of different issues directly related to their condition, which range from physical limitations and uncertainty over their diagnosis, which in some cases cause significant depression and anxiety, to impact on their relationships with friends and family, financial challenges and family planning.In this article, we interview two patients living with PAH-CHD and discuss the numerous issues that patients may face as a direct result of their condition. Pulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension associated with Congenital Heart Disease (PAH-CHD) face a number of different issues directly related to their condition, which range from physical limitations and uncertainty over their diagnosis, which in some cases cause significant depression and anxiety, to impact on their relationships with friends and family, financial challenges and family planning. In this article, we interview two patients living with PAH-CHD and discuss the numerous issues that patients may face as a direct result of their condition. Pulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension associated with Congenital Heart Disease (PAH-CHD) face a number of different issues directly related to their condition, which range from physical limitations and uncertainty over their diagnosis, which in some cases cause significant depression and anxiety, to impact on their relationships with friends and family, financial challenges and family planning. In this article, we interview two patients living with PAH-CHD and discuss the numerous issues that patients may face as a direct result of their condition.Pulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension associated with Congenital Heart Disease (PAH-CHD) face a number of different issues directly related to their condition, which range from physical limitations and uncertainty over their diagnosis, which in some cases cause significant depression and anxiety, to impact on their relationships with friends and family, financial challenges and family planning. In this article, we interview two patients living with PAH-CHD and discuss the numerous issues that patients may face as a direct result of their condition. AbstractPulmonary Hypertension is a serious condition which can occur in adults living with congenital heart disease. Due to advances in the care of patients with congenital heart disease, patients are living longer with the condition. Unfortunately, patients living with Pulmonary Arterial Hypertension associated with Congenital Heart Disease (PAH-CHD) face a number of different issues directly related to their condition, which range from physical limitations and uncertainty over their diagnosis, which in some cases cause significant depression and anxiety, to impact on their relationships with friends and family, financial challenges and family planning. In this article, we interview two patients living with PAH-CHD and discuss the numerous issues that patients may face as a direct result of their condition. |
| ArticleNumber | 100596 |
| Author | Howard, Luke S. Jeffery, Daniel A. Gin-Sing, Wendy Bedair, Radwa |
| Author_xml | – sequence: 1 givenname: Daniel A. surname: Jeffery fullname: Jeffery, Daniel A. organization: Morriston Cardiac Centre, Swansea Bay University Healthboard, Swansea, SA6 6NL, UK – sequence: 2 givenname: Wendy surname: Gin-Sing fullname: Gin-Sing, Wendy organization: National Pulmonary Hypertension Service, Hammersmith Hospital, Imperial College Healthcare Trust, London, W12 0HS, UK – sequence: 3 givenname: Radwa surname: Bedair fullname: Bedair, Radwa organization: Bristol Heart Institute, Bristol Royal Infirmary, Bristol, BS2 8HW, UK – sequence: 4 givenname: Luke S. orcidid: 0000-0003-2822-210X surname: Howard fullname: Howard, Luke S. email: l.howard@imperial.ac.uk organization: National Pulmonary Hypertension Service, Hammersmith Hospital, Imperial College Healthcare Trust, London, W12 0HS, UK |
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| Cites_doi | 10.1186/1465-9921-14-104 10.1016/S0735-1097(98)00162-4 10.1097/MD.0000000000020285 10.1001/archinte.161.15.1849 10.1513/AnnalsATS.202208-721RL 10.1186/1477-7525-11-161 10.1086/677365 10.1177/0269216311407694 10.1111/j.1471-0528.2009.02492.x 10.1136/bmjopen-2013-004735 10.1164/rccm.202010-3967LE 10.1183/09031936.00141211 10.1111/chd.12638 10.1183/13993003.00879-2022 10.1183/09031936.00127113 10.1093/eurheartj/ehv317 10.1080/14779072.2019.1550716 10.1016/j.ijcard.2014.04.072 10.1007/s11136-005-3513-4 10.1002/ehf2.13263 10.1093/eurheartj/ehn597 10.1136/bmjresp-2021-000876 10.1016/S0033-3182(10)70706-4 10.1186/s12931-016-0388-6 10.1183/13993003.01129-2024 10.1183/13993003.01180-2024 10.1016/j.amjcard.2009.01.021 10.3389/fmed.2022.765461 10.1183/13993003.00124-2020 |
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| Keywords | Adult congenital heart disease Pulmonary arterial hypertension Quality of life |
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| Title | The PAH patient's perspective |
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