Cystic Fibrosis‐related Liver Disease is Associated With Increased Disease Burden and Endocrine Comorbidities

• Published in: Journal of pediatric gastroenterology and nutrition Vol. 70; no. 6; pp. 796 - 800
• Main Authors: Singh, Harveen, Coffey, Michael J., Ooi, Chee Y.
• Format: Journal Article
• Language: English
• Published: United States by European Society for Pediatric Gastroenterology, Hepatology, and Nutrition and North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition 01.06.2020; by European Society for Pediatric Gastroenterology, Hepatology, and Nutrition and North American Society for Pediatric Gastroenterology
• Subjects: cystic fibrosis; cystic fibrosis liver disease; pancreatic insufficiency

ABSTRACT Background: Cystic fibrosis‐related liver disease (CFLD) is the leading nonpulmonary cause of mortality in cystic fibrosis (CF). We evaluated and compared the burden of disease and nonrespiratory comorbidities of those with severe CFLD and those without (noCFLD). Methods: A retrospective na...