Updated Clinical Classification of Pulmonary Hypertension

• Published in: Journal of the American College of Cardiology Vol. 54; no. 1; pp. S43 - S54
• Main Authors: Simonneau, Gérald, Robbins, Ivan M., Beghetti, Maurice, Channick, Richard N., Delcroix, Marion, Denton, Christopher P., Elliott, C. Gregory, Gaine, Sean P., Gladwin, Mark T., Jing, Zhi-Cheng, Krowka, Michael J., Langleben, David, Nakanishi, Norifumi, Souza, Rogério
• Format: Journal Article
• Language: English
• Published: United States Elsevier Inc 30.06.2009; Elsevier Limited
• Subjects: Algorithms; Anticoagulants - therapeutic use; Antihypertensive Agents - administration & dosage; Calcium Channel Blockers - therapeutic use; Cardiology; Cardiovascular; Cardiovascular disease; Classification; clinical classification; Clinical trials; Comorbidity; Defects; Drug therapy; Endothelin Receptor Antagonists; Epoprostenol - administration & dosage; Evidence-Based Medicine; Family medical history; Genetic counseling; Humans; Hypertension, Pulmonary - classification; Hypertension, Pulmonary - drug therapy; Hypertension, Pulmonary - epidemiology; Internal Medicine; Mutation; Prognosis; pulmonary arterial hypertension; Pulmonary hypertension; Randomized Controlled Trials as Topic; Scleroderma, Systemic - epidemiology; Surgery; Treatment Outcome; United States > US; California; ESRD; BMPR2; OR; pulmonary hypertension; PPH; IPAH; PVR; POPH; HIV; PCH; SCD; PAH; PH; clinical classification; TRV; CTEPH; pulmonary arterial hypertension; CHD; PAP; PVOD; odds ratio; pulmonary arterial pressure; primary pulmonary hypertension; sickle cell disease; congenital heart disease; bone morphogenetic protein receptor type 2; tricuspid regurgitation jet velocity; end-stage renal disease; idiopathic pulmonary arterial hypertension; chronic thromboembolic pulmonary hypertension; human immunodeficiency virus; pulmonary veno-occlusive disease; pulmonary vascular resistance; pulmonary capillary hemangiomatosis; portopulmonary hypertension

The aim of a clinical classification of pulmonary hypertension (PH) is to group together different manifestations of disease sharing similarities in pathophysiologic mechanisms, clinical presentation, and therapeutic approaches. In 2003, during the 3rd World Symposium on Pulmonary Hypertension, the...