Behavioral features of Williams Beuren syndrome compared to Fragile X syndrome and subjects with intellectual disability without defined etiology

• Published in: Research in developmental disabilities Vol. 32; no. 2; pp. 643 - 652
• Main Authors: Pérez-García, D., Granero, R., Gallastegui, F., Pérez-Jurado, L.A., Brun-Gasca, C.
• Format: Journal Article
• Language: English
• Published: Amsterdam Elsevier Ltd 01.03.2011; Elsevier
• Subjects: Adolescent; Adult; Adult and adolescent clinical studies; Aetiology; Aggression; Anxiety; Anxiety Disorders - etiology; Anxiety Disorders - psychology; Anxiety-Depression; Behavior Problems; Behavioral phenotype; Biological and medical sciences; Check Lists; Child; Child Behavior; Child Behavior Checklist; Child Behavior Disorders - etiology; Child Behavior Disorders - psychology; Child clinical studies; Child, Preschool; Chromosome aberrations; Chromosome fragility (bloom syndrome, ataxia telangiectasia, fanconi anemia, x-linked mental retardation...); Cognitive Processes; Delinquency; Depression (Psychology); Depressive Disorder - etiology; Depressive Disorder - psychology; Developmental Disabilities; Developmental disorders; Etiology; Female; Fragile X syndrome; Fragile X Syndrome - complications; Fragile X Syndrome - psychology; Gender Differences; Genetic Disorders; Humans; Intellectual deficiency; Intellectual disability; Intellectual Disability - complications; Intellectual Disability - etiology; Intellectual Disability - psychology; Intelligence; Intelligence Quotient; Learning disabilities; Male; Medical genetics; Medical sciences; Mental Retardation; Neurological Impairments; Phenotype; Phenotypes; Psychology. Psychoanalysis. Psychiatry; Psychopathology; Psychopathology. Psychiatry; Symptoms (Individual Disorders); Williams Syndrome - complications; Williams Syndrome - genetics; Williams Syndrome - psychology; Williams-Beuren syndrome; Young Adult; IQ; Anxiety; Intellectual disability; Fragile X syndrome; Williams-Beuren syndrome; Behavioral phenotype; Chromosomal aberration; Chromosome fragility; Anxiety disorder; Cognition; Developmental disorder; Mental retardation; Behavioral analysis; Etiology; Intellectual ability; Child; Human; Preschool age; Handicap; Williams syndrome; Phenotype; School age; Adolescent; Young adult; Intellectual deficiency; Intelligence quotient

▶ Definition the psychopathological profile of WBS in comparison to FXS and IDNS. ▶ High prevalence of anxiety, depression and attention problems in WBS. ▶ Delinquent and aggressive behaviors and externalizing problems are rare in WBS patients. ▶ Behavioral problems are secondary to the intellectual...