Adult case of large sinonasal embryonal rhabdomyosarcoma with intracranial extension
The main histologic types are embryonal (71%) and alveolar (13%).3 They usually carry a poor prognosis due to skull base and intracranial extension.4 They also have the potential for cerebrospinal fluid dissemination, as well as distant metastasis to the lungs, cervical lymph nodes, and bones.4'...
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Published in | Ear, nose, & throat journal Vol. 92; no. 4-5; pp. 177 - 178 |
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Main Authors | , , , , |
Format | Journal Article |
Language | English |
Published |
United States
Sage Publications, Inc
01.04.2013
SAGE PUBLICATIONS, INC |
Subjects | |
Online Access | Get full text |
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Summary: | The main histologic types are embryonal (71%) and alveolar (13%).3 They usually carry a poor prognosis due to skull base and intracranial extension.4 They also have the potential for cerebrospinal fluid dissemination, as well as distant metastasis to the lungs, cervical lymph nodes, and bones.4'6 Imaging of RMS with CT and MRI is essential for diagnosis and for the evaluation of the high rate of metastatic disease.4 Despite great advances in therapy, only a small increase in the 5-year survival rate for adult RMS has been shown.7 A good response was attained in our patient, perhaps because the tumor was of the embryonal type, and because of the multimodality therapy, resulting in an apparent complete remission of the tumor. |
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Bibliography: | ObjectType-Case Study-2 SourceType-Scholarly Journals-1 ObjectType-Feature-4 content type line 23 ObjectType-Report-1 ObjectType-Article-3 |
ISSN: | 0145-5613 1942-7522 |
DOI: | 10.1177/014556131309200406 |