Survival in scleroderma: results from the population-based South Australian Register

• Published in: Internal medicine journal Vol. 41; no. 5; pp. 381 - 390
• Main Authors: Hissaria, P., Lester, S., Hakendorf, P., Woodman, R., Patterson, K., Hill, C., Ahern, M. J., Smith, M. D., Walker, J. G., Roberts-Thomson, P. J.
• Format: Journal Article
• Language: English
• Published: Melbourne, Australia Blackwell Publishing Asia 01.05.2011
• Subjects: Adult; Age of Onset; Aged; Autoantibodies - blood; Autoantigens - immunology; Comorbidity; end-organ involvement; Female; Humans; Hypertension, Pulmonary - etiology; Hypertension, Pulmonary - mortality; Kaplan-Meier Estimate; Kidney Failure, Chronic - etiology; Kidney Failure, Chronic - mortality; Male; Microscopic Angioscopy; Middle Aged; mortality; nailfold capillaroscopy; Nails - blood supply; Neoplasms - epidemiology; Proportional Hazards Models; Pulmonary Fibrosis - etiology; Pulmonary Fibrosis - mortality; Registries; Retrospective Studies; scleroderma; Scleroderma, Diffuse - complications; Scleroderma, Diffuse - immunology; Scleroderma, Diffuse - mortality; Scleroderma, Diffuse - pathology; Sex Factors; South Australia - epidemiology; survival; South Australia

Aim:  To ascertain the mortality risk and investigate clinical and serological factors influencing survival of patients listed on the South Australian Scleroderma Register (SASR). Methods:  The SASR is a population‐based register, which was commenced in 1993 and has actively sought to recruit all sc...