Skin manifestations in autoinflammatory syndromes

• Published in: Journal der Deutschen Dermatologischen Gesellschaft Vol. 9; no. 3; pp. 232 - 245
• Main Authors: Braun-Falco, Markus, Ruzicka, Thomas
• Format: Journal Article
• Language: English
• Published: Oxford, UK Blackwell Publishing Ltd 01.03.2011
• Subjects: CAPS; Hereditary Autoinflammatory Diseases - complications; Hereditary Autoinflammatory Diseases - diagnosis; Hereditary Autoinflammatory Diseases - therapy; Humans; inflammasome; interleukin-1; Mediterranean fever; PAPA syndrome; periodic fever syndromes; Schnitzler syndrome; Skin Diseases - diagnosis; Skin Diseases - etiology; Skin Diseases - therapy; Syndrome

Summary Autoinflammatory diseases encompass a group of inflammatory diseases that are non‐infectious, non‐allergic, non‐autoimmune and non‐immunodeficient. The term was initially coined for a small group of familial periodic fever syndromes of which familial Mediterranean fever (FMF) is the most com...