Successful Surgical Repair of Type A Acute Aortic Dissection in a Patient with Vascular Ehlers–Danlos Syndrome

• Published in: Annals of Vascular Diseases Vol. 15; no. 1; pp. 58 - 61
• Main Authors: Mori, Kousuke, Ishii, Hirohito, Sakaguchi, Shuhei, Sakurahara, Daichi, Iwasaki, Ayaka, Furukawa, Koji
• Format: Journal Article
• Language: English
• Published: Japan The Editorial Committee of Annals of Vascular Diseases 25.03.2022; Japanese College of Angiology / The Japanese Society for Vascular Surgery / Japanese Society of Phlebology
• Subjects: Case Report; total arch replacement; type A acute aortic dissection; vascular Ehlers–Danlos syndrome; total arch replacement; vascular Ehlers–Danlos syndrome; type A acute aortic dissection

Surgery for vascular complications of a patient with vascular Ehlers–Danlos syndrome (vEDS) is challenging due to the fragility of the associated tissues. In this study, we present a type A acute aortic dissection case in a patient with vEDS successfully treated via total arch replacement. A 42-year...