Disability and quality of life in hereditary ataxias: a self-administered postal questionnaire

A postal questionnaire was sent to 151 patients affected by Friedreich's disease (FD) and other hereditary ataxias (OHA) to study their disability and quality of life. A 79.5% response rate was obtained. A scoring system based on disability in walking, dressing, personal care, eating and speaki...

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Published inInternational disability studies Vol. 9; no. 1; p. 10
Main Authors D'Ambrosio, R, Leone, M, Rosso, M G, Mittino, D, Brignolio, F
Format Journal Article
LanguageEnglish
Published Switzerland 1987
Subjects
Activities of Daily Living
Adolescent
Adult
Child
Disabled Persons
Female
Friedreich Ataxia - genetics
Friedreich Ataxia - physiopathology
Friedreich Ataxia - psychology
Gait
Humans
Italy
Male
Middle Aged
Postal Service
Prognosis
Quality of Life
Self Disclosure
Social Support
Surveys and Questionnaires
Italy
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Abstract A postal questionnaire was sent to 151 patients affected by Friedreich's disease (FD) and other hereditary ataxias (OHA) to study their disability and quality of life. A 79.5% response rate was obtained. A scoring system based on disability in walking, dressing, personal care, eating and speaking was developed and used. Walking was the most impaired activity. The degree of disability was similar between FD and OHA. Institutionalization, frequency of social contacts, work activity, recreational and social activities were influenced by disability.
AbstractList A postal questionnaire was sent to 151 patients affected by Friedreich's disease (FD) and other hereditary ataxias (OHA) to study their disability and quality of life. A 79.5% response rate was obtained. A scoring system based on disability in walking, dressing, personal care, eating and speaking was developed and used. Walking was the most impaired activity. The degree of disability was similar between FD and OHA. Institutionalization, frequency of social contacts, work activity, recreational and social activities were influenced by disability.
Author Brignolio, F
Leone, M
Mittino, D
Rosso, M G
D'Ambrosio, R
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  fullname: Brignolio, F
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Snippet A postal questionnaire was sent to 151 patients affected by Friedreich's disease (FD) and other hereditary ataxias (OHA) to study their disability and quality...
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StartPage 10
SubjectTerms Activities of Daily Living
Adolescent
Adult
Child
Disabled Persons
Female
Friedreich Ataxia - genetics
Friedreich Ataxia - physiopathology
Friedreich Ataxia - psychology
Gait
Humans
Italy
Male
Middle Aged
Postal Service
Prognosis
Quality of Life
Self Disclosure
Social Support
Surveys and Questionnaires
Title Disability and quality of life in hereditary ataxias: a self-administered postal questionnaire
URI https://www.ncbi.nlm.nih.gov/pubmed/2959645
Volume 9
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