Sarcoidosis-associated pulmonary hypertension: a role for endothelin receptor antagonists?

• Published in: Therapeutic advances in respiratory disease Vol. 3; no. 3; pp. 99 - 101
• Main Authors: Pitsiou, Georgia G., Spyratos, Dionysis, Kioumis, Ioannis, Boutou, Afroditi K., Nakou, Chrysanthi, Stanopoulos, Ioannis
• Format: Journal Article
• Language: English
• Published: London, England SAGE Publications 01.06.2009; SAGE PUBLICATIONS, INC; SAGE Publishing
• Subjects: Endothelin Receptor Antagonists; Humans; Hypertension, Pulmonary - drug therapy; Hypertension, Pulmonary - etiology; Male; Middle Aged; Pulmonary hypertension; Sarcoidosis; Sarcoidosis, Pulmonary - complications; Sulfonamides - therapeutic use; bosentan; pulmonary hypertension; sarcoidosis

Data on the treatment of sarcoidosis-associated pulmonary hypertension are scarce, while the variety of underlying pathophysiologic mechanisms are a major limitation in the implementation of a universal therapy. We report a 47-year-old male patient who presented with stage II sarcoidosis and associa...