Perioperative anesthetic management of children with congenital central hypoventilation syndrome and rapid‐onset obesity with hypothalamic dysfunction, hypoventilation, and autonomic dysregulation undergoing thoracoscopic phrenic nerve‐diaphragm pacemaker implantation

• Published in: Pediatric anesthesia Vol. 28; no. 11; pp. 963 - 973
• Main Authors: Ballard, Heather A., Leavitt, Olga S., Chin, Anthony C., Kabre, Rashmi, Weese‐Mayer, Debra E., Hajduk, John, Jagannathan, Narasimhan
• Format: Journal Article
• Language: English
• Published: France Wiley Subscription Services, Inc 01.11.2018
• Subjects: Adolescent; Anesthesia - methods; Anesthetics - therapeutic use; autonomic dysregulation; central sleep apnea; Child; Child, Preschool; Congenital Central Hypoventilation Syndrome; Diaphragm - surgery; Electric Stimulation Therapy - methods; Humans; Hypothalamic Diseases - physiopathology; hypoventilation; Hypoventilation - congenital; Hypoventilation - physiopathology; Hypoventilation - therapy; Infant; Narcotics; Obesity; one‐lung ventilation; Ostomy; pacemaker; Pacemaker, Artificial; Pain; Patients; Pediatric Obesity - physiopathology; Perioperative Care - methods; phrenic nerve; Phrenic Nerve - surgery; rapid‐onset obesity with hypothalamic dysfunction; Retrospective Studies; Sleep apnea; Sleep Apnea, Central - physiopathology; Sleep Apnea, Central - therapy; Syndrome; Tracheostomy; Ventilators; Congenital Central Hypoventilation Syndrome; pacemaker; phrenic nerve; rapid-onset obesity with hypothalamic dysfunction; central sleep apnea; hypoventilation; one-lung ventilation; autonomic dysregulation

Summary Background Congenital Central Hypoventilation Syndrome and Rapid‐Onset Obesity with Hypothalamic dysfunction, Hypoventilation, and Autonomic Dysregulation are rare neurocristopathies characterized by autonomic dysregulation including bradyarrhythmias, abnormal temperature control, and most s...