Perioperative management of familial dysautonomia: a systematic review

• Published in: European journal of anaesthesiology Vol. 24; no. 4; p. 309
• Main Authors: Weingarten, T N, Sprung, J, Burgher, A H
• Format: Journal Article
• Language: English
• Published: England 01.04.2007
• Subjects: Anesthesia - methods; Blood Pressure; Dysautonomia, Familial - complications; Dysautonomia, Familial - physiopathology; Gastrointestinal Diseases - therapy; Humans; Lung Diseases - therapy; Perioperative Care; Postoperative Complications - prevention & control

Familial dysautonomia (FD), a rare genetic disorder, is characterized by autonomic instability, pulmonary infections, oesophageal dysmotility, spinal abnormalities and episodic "dysautonomic crisis" characterized by rash, vomiting, sweating and hypertension. Frequent anaesthetic complicati...