Treatment of a direct carotid-cavernous fistula in a patient with type IV Ehlers-Danlos syndrome : a novel approach

• Published in: Neuroradiology Vol. 48; no. 7; pp. 491 - 494
• Main Authors: HOLLANDS, J. K, SANTARIUS, T, KIRKPATRICK, P. J, HIGGINS, J. N
• Format: Journal Article
• Language: English
• Published: Berlin Springer 01.07.2006; Springer Nature B.V
• Subjects: Adult; Angioplasty, Balloon - methods; Biological and medical sciences; Blood vessels; Carotid-Cavernous Sinus Fistula - complications; Carotid-Cavernous Sinus Fistula - diagnosis; Carotid-Cavernous Sinus Fistula - therapy; Case studies; Chromosome aberrations; Ehlers-Danlos Syndrome - complications; Embolization, Therapeutic - methods; Female; Genetic disorders; Headache. Facial pains. Syncopes. Epilepsia. Intracranial hypertension. Brain oedema. Cerebral palsy; Humans; Investigative techniques, diagnostic techniques (general aspects); Medical genetics; Medical procedures; Medical sciences; Nervous system; Nervous system (semeiology, syndromes); Neurology; Radiodiagnosis. Nmr imagery. Nmr spectrometry; Human; Skin disease; Nervous system diseases; Ehlers-Danlos syndrome; Elastic tissue disease; Radiodiagnosis; Diseases of the osteoarticular system; Artery; Genetic disease; Treatment; Blood vessel; Carotid; Ehlers Danlos syndrome; Systemic disease; Carotid-cavernous fistula; Surgical approach; Circulatory system

We report a case of a 34-year-old female with type IV Ehlers-Danlos syndrome diagnosed with a carotid cavernous fistula presenting with progressive proptosis. Endovascular embolization using balloons or coils carries a high risk of complications in this group of patients, owing to the extreme fragil...