Successful case report of congenital long-segment complex tracheal stenosis treated with sliding tracheoplasty associated with pulmonary artery vascular ring

• Published in: The Gazette of the Egyptian Paediatric Association Vol. 72; no. 1; pp. 55 - 6
• Main Authors: Cirerol, Enrique R. Leal, Fol, Jose Mora, Valdez, Carlos Max Luna, Osta, David Arellano, Nájera, Jorge Fonseca, Ubaldo, Jesús Monroy, González, María Magdalena Ramírez, Guerrero, Valery Selene Valadez, Brenes Guzmán, Sofia
• Format: Journal Article
• Language: English
• Published: Berlin/Heidelberg Springer Berlin Heidelberg 01.12.2024; Springer; Springer Nature B.V; SpringerOpen
• Subjects: Bronchoscopy; Cardiac patients; Cardiology; Case Report; Case reports; Communication; Congenital heart disease; Coronary vessels; Cyanosis; Diseases; Heart defects; Heart diseases; Heart surgery; Medicine; Medicine & Public Health; Mexico; Patients; Pediatric; Pediatrics; Pneumonia; Pulmonary arteries; Pulmonary hypertension; Stenosis; Sutures; Thoracic surgery; Trachea; Tracheal stenosis; Veins & arteries; Ventilators; Mexico; Tracheal stenosis; Heart defects; Case report; Pediatric
• ISSN: 2090-9942; 1110-6638; 2090-9942
• DOI: 10.1186/s43054-024-00296-w

Background Congenital tracheal stenosis is a rare structural obstructive disorder affecting a segment of the trachea. It is often caused by complete or nearly complete cartilaginous rings narrowing the airway. Approximately 50% of cases are associated with abnormal left pulmonary artery rings. Case presentation We present the case of a 4-month-old female infant with complex congenital tracheal stenosis associated with a left pulmonary artery vascular ring and congenital heart disease. The patient underwent successful surgical intervention involving repair of the congenital heart defect and reimplantation of the pulmonary artery, followed by sliding tracheoplasty in one surgery procedure. Postoperative outcomes were favorable, with successful extubating and resolution of respiratory symptoms. Conclusions Sliding tracheoplasty proved an effective treatment option in this complex case, highlighting its reproducibility and favorable outcomes in managing congenital tracheal stenosis.