LeFort III/I for Beckwith-Wiedemann Syndrome: A Case Report

This case presents a facially mature patient with Beckwith-Wiedemann Syndrome (BWS) who presented with severe class III malocclusion. Computed tomography imaging revealed an anterior crossbite of 19 mm and a narrow pharyngeal airway at the level of the tongue base precluding mandibular setback surge...

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Bibliographic Details
Published inThe Cleft palate-craniofacial journal p. 10556656221101776
Main Authors Muller, John N, Shetye, Pradip R, Flores, Roberto L
Format Journal Article
LanguageEnglish
Published United States 01.10.2023
Subjects
midfacial growth
surgical technique
osteotomy
dental occlusion
maxilla
mandible
orthognathic surgery
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Summary:This case presents a facially mature patient with Beckwith-Wiedemann Syndrome (BWS) who presented with severe class III malocclusion. Computed tomography imaging revealed an anterior crossbite of 19 mm and a narrow pharyngeal airway at the level of the tongue base precluding mandibular setback surgery. The patient was indicated for a LeFort III combined with a LeFort I advancement, each of 10 mm, for a 20 mm combined advancement. Stable, functional occlusion was achieved without airway compromise. This novel use of the combined LeFort III/I can restore stable class I occlusion in patients with BWS at risk for tongue base airway compromise.
ISSN:1545-1569
DOI:10.1177/10556656221101776