26-Year-Old Survivor of Kasai Procedure With Native Liver

A 26-year old woman with history of congenital biliary atresia and Kasai procedure as a newborn presented with recurrent nausea and abdominal pain. Physical examination showed anicteric sclera and tender right upper quadrant. Elevated liver function tests suggested obstruction and hepatitis. Percuta...

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Published inACG case reports journal Vol. 3; no. 3; pp. 221 - 223
Main Authors Omar, Hina, Siglin, Scott, Laurie, Timothy, Kavin, Hymie
Format Journal Article
LanguageEnglish
Published United States American College of Gastroenterology 01.04.2016
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Case Report
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Abstract A 26-year old woman with history of congenital biliary atresia and Kasai procedure as a newborn presented with recurrent nausea and abdominal pain. Physical examination showed anicteric sclera and tender right upper quadrant. Elevated liver function tests suggested obstruction and hepatitis. Percutaneous transhepatic cholangiogram showed generalized ductal dilation, innumerable intrahepatic bile duct stones, and multiple filling defects. No anastomotic stenosis was noted. The patient was treated for acute symptoms and referred to a liver transplant center. Long-term survivors of the Kasai procedure with a native liver are rare, and this represents the third known U.S. case in the literature.
AbstractList A 26-year old woman with history of congenital biliary atresia and Kasai procedure as a newborn presented with recurrent nausea and abdominal pain. Physical examination showed anicteric sclera and tender right upper quadrant. Elevated liver function tests suggested obstruction and hepatitis. Percutaneous transhepatic cholangiogram showed generalized ductal dilation, innumerable intrahepatic bile duct stones, and multiple filling defects. No anastomotic stenosis was noted. The patient was treated for acute symptoms and referred to a liver transplant center. Long-term survivors of the Kasai procedure with a native liver are rare, and this represents the third known U.S. case in the literature.
Author Laurie, Timothy
Kavin, Hymie
Siglin, Scott
Omar, Hina
AuthorAffiliation 1 Division of Internal Medicine, Advocate Lutheran General Hospital, Park Ridge, IL
2 Division of Gastroenterology, Advocate Lutheran General Hospital, Park Ridge, IL
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  givenname: Hymie
  surname: Kavin
  fullname: Kavin, Hymie
  organization: Division of Gastroenterology, Advocate Lutheran General Hospital, Park Ridge, IL
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Cites_doi 10.1016/0022-3468(91)90903-7
10.1097/MPG.0b013e318189f2d5
10.1203/01.PDR.0000159569.57354.47
10.4174/jkss.2011.81.4.271
10.1002/hep.20547
10.1097/01.mpg.0000189339.92891.64
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Snippet A 26-year old woman with history of congenital biliary atresia and Kasai procedure as a newborn presented with recurrent nausea and abdominal pain. Physical...
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Title 26-Year-Old Survivor of Kasai Procedure With Native Liver
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