Tetrahydrobiopterin shifts the balance from oxidative stress to NO signalling in Duchenne muscular dystrophy
Wuebbles, Ryan D, Oliveira-Santos, Ariany, Burkin, Dean J
Published in Acta Physiologica (01.07.2021)
Published in Acta Physiologica (01.07.2021)
Get full text
Journal Article
Laminin-111 protein therapy enhances muscle regeneration and repair in the GRMD dog model of Duchenne muscular dystrophy
Barraza-Flores, Pamela, Fontelonga, Tatiana M, Wuebbles, Ryan D, Hermann, Hailey J, Nunes, Andreia M, Kornegay, Joe N, Burkin, Dean J
Published in Human molecular genetics (15.08.2019)
Published in Human molecular genetics (15.08.2019)
Get full text
Journal Article
A gene therapy approach for the treatment of limb-girdle muscular dystrophy 2C/R5
Hermann, Hailey, Wuebbles, Ryan D., Burkin, Dean J.
Published in Molecular therapy. Methods & clinical development (08.06.2023)
Published in Molecular therapy. Methods & clinical development (08.06.2023)
Get full text
Journal Article
Laminin-111 Protein Therapy Reduces Muscle Pathology and Improves Viability of a Mouse Model of Merosin-Deficient Congenital Muscular Dystrophy
Rooney, Jachinta E, Knapp, Jolie R, Hodges, Bradley L, Wuebbles, Ryan D, Burkin, Dean J
Published in The American journal of pathology (01.04.2012)
Published in The American journal of pathology (01.04.2012)
Get full text
Journal Article
Impaired fetal muscle development and JAK-STAT activation mark disease onset and progression in a mouse model for merosin-deficient congenital muscular dystrophy
Nunes, Andreia M, Wuebbles, Ryan D, Sarathy, Apurva, Fontelonga, Tatiana M, Deries, Marianne, Burkin, Dean J, Thorsteinsdóttir, Sólveig
Published in Human molecular genetics (01.06.2017)
Published in Human molecular genetics (01.06.2017)
Get full text
Journal Article
Sunitinib promotes myogenic regeneration and mitigates disease progression in the mdx mouse model of Duchenne muscular dystrophy
Fontelonga, Tatiana M, Jordan, Brennan, Nunes, Andreia M, Barraza-Flores, Pamela, Bolden, Nicholas, Wuebbles, Ryan D, Griner, Lesley Mathews, Hu, Xin, Ferrer, Marc, Marugan, Juan, Southall, Noel, Burkin, Dean J
Published in Human molecular genetics (01.07.2019)
Published in Human molecular genetics (01.07.2019)
Get full text
Journal Article
Transgenic mice expressing tunable levels of DUX4 develop characteristic facioscapulohumeral muscular dystrophy-like pathophysiology ranging in severity
Jones, Takako I, Chew, Guo-Liang, Barraza-Flores, Pamela, Schreier, Spencer, Ramirez, Monique, Wuebbles, Ryan D, Burkin, Dean J, Bradley, Robert K, Jones, Peter L
Published in Skeletal muscle (11.04.2020)
Published in Skeletal muscle (11.04.2020)
Get full text
Journal Article
Transgenic overexpression of α7 integrin in smooth muscle attenuates allergen‐induced airway inflammation in a murine model of asthma
Ba, Mariam A., Aiyuk, Annemarie, Hernández, Karla, Evasovic, Jon M., Wuebbles, Ryan D., Burkin, Dean J., Singer, Cherie A.
Published in FASEB bioAdvances (01.11.2022)
Published in FASEB bioAdvances (01.11.2022)
Get full text
Journal Article
SU9516 Increases α7β1 Integrin and Ameliorates Disease Progression in the mdx Mouse Model of Duchenne Muscular Dystrophy
Sarathy, Apurva, Wuebbles, Ryan D., Fontelonga, Tatiana M., Tarchione, Ashley R., Mathews Griner, Lesley A., Heredia, Dante J., Nunes, Andreia M., Duan, Suzann, Brewer, Paul D., Van Ry, Tyler, Hennig, Grant W., Gould, Thomas W., Dulcey, Andrés E., Wang, Amy, Xu, Xin, Chen, Catherine Z., Hu, Xin, Zheng, Wei, Southall, Noel, Ferrer, Marc, Marugan, Juan, Burkin, Dean J.
Published in Molecular therapy (07.06.2017)
Published in Molecular therapy (07.06.2017)
Get full text
Journal Article
Transgenic overexpression of the α7 integrin reduces muscle pathology and improves viability in the dy(W) mouse model of merosin-deficient congenital muscular dystrophy type 1A
Doe, Jinger A, Wuebbles, Ryan D, Allred, Erika T, Rooney, Jachinta E, Elorza, Margaret, Burkin, Dean J
Published in Journal of cell science (01.07.2011)
Published in Journal of cell science (01.07.2011)
Get full text
Journal Article
Muscular dystrophy candidate gene FRG1 is critical for muscle development
Hanel, Meredith L., Wuebbles, Ryan D., Jones, Peter L.
Published in Developmental dynamics (01.06.2009)
Published in Developmental dynamics (01.06.2009)
Get full text
Journal Article
Human Galectin-1 Improves Sarcolemma Stability and Muscle Vascularization in the mdx Mouse Model of Duchenne Muscular Dystrophy
Wuebbles, Ryan D., Cruz, Vivian, Van Ry, Pam, Barraza-Flores, Pamela, Brewer, Paul D., Jones, Peter, Burkin, Dean J.
Published in Molecular therapy. Methods & clinical development (14.06.2019)
Published in Molecular therapy. Methods & clinical development (14.06.2019)
Get full text
Journal Article
Levels of α7 integrin and laminin-α2 are increased following prednisone treatment in the mdx mouse and GRMD dog models of Duchenne muscular dystrophy
Wuebbles, Ryan D, Sarathy, Apurva, Kornegay, Joe N, Burkin, Dean J
Published in Disease models & mechanisms (01.09.2013)
Published in Disease models & mechanisms (01.09.2013)
Get full text
Journal Article
Transgenic overexpression of the α7 integrin reduces muscle pathology and improves viability in the dyW mouse model of merosin-deficient congenital muscular dystrophy type 1A
Doe, Jinger A., Wuebbles, Ryan D., Allred, Erika T., Rooney, Jachinta E., Elorza, Margaret, Burkin, Dean J.
Published in Journal of cell science (01.07.2011)
Published in Journal of cell science (01.07.2011)
Get full text
Journal Article