EL20, a potent antiarrhythmic compound, selectively inhibits calmodulin-deficient ryanodine receptor type 2
Klipp, Robert C., Li, Na, Wang, Qiongling, Word, Tarah A., Sibrian-Vazquez, Martha, Strongin, Robert M., Wehrens, Xander H.T., Abramson, Jonathan J.
Published in Heart rhythm (01.04.2018)
Published in Heart rhythm (01.04.2018)
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Journal Article
Treatment of catecholaminergic polymorphic ventricular tachycardia in mice using novel RyR2 - modifying drugs
Li, Na, Wang, Qiongling, Sibrian-Vazquez, Martha, Klipp, Robert C, Reynolds, Julia O, Word, Tarah A, Scott, Larry, Salama, Guy, Strongin, Robert M, Abramson, Jonathan J, Wehrens, Xander H.T
Published in International journal of cardiology (15.01.2017)
Published in International journal of cardiology (15.01.2017)
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Journal Article
Targeting pathological leak of ryanodine receptors: preclinical progress and the potential impact on treatments for cardiac arrhythmias and heart failure
Connell, Patrick, Word, Tarah A, Wehrens, Xander H T
Published in Expert opinion on therapeutic targets (02.01.2020)
Published in Expert opinion on therapeutic targets (02.01.2020)
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Journal Article
Loss of SPEG Inhibitory Phosphorylation of Ryanodine Receptor Type-2 Promotes Atrial Fibrillation
Campbell, Hannah M, Quick, Ann P, Abu-Taha, Issam, Chiang, David Y, Kramm, Carlos F, Word, Tarah A, Brandenburg, Sören, Hulsurkar, Mohit, Alsina, Katherina M, Liu, Hui-Bin, Martin, Brian, Uhlenkamp, Dennis, Moore, Oliver M, Lahiri, Satadru K, Corradini, Eleonora, Kamler, Markus, Heck, Albert J.R, Lehnart, Stephan E, Dobrev, Dobromir, Wehrens, Xander H.T
Published in Circulation (New York, N.Y.) (22.09.2020)
Published in Circulation (New York, N.Y.) (22.09.2020)
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Journal Article
In Vivo Ryr2 Editing Corrects Catecholaminergic Polymorphic Ventricular Tachycardia
Pan, Xiaolu, Philippen, Leonne, Lahiri, Satadru K, Lee, Ciaran, Park, So Hyun, Word, Tarah A, Li, Na, Jarrett, Kelsey E, Gupta, Rajat, Reynolds, Julia O, Lin, Jean, Bao, Gang, Lagor, William R, Wehrens, Xander H.T
Published in Circulation research (28.09.2018)
Published in Circulation research (28.09.2018)
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Journal Article
Loss of Protein Phosphatase 1 Regulatory Subunit PPP1R3A Promotes Atrial Fibrillation
Alsina, Katherina M, Hulsurkar, Mohit, Brandenburg, Sören, Kownatzki-Danger, Daniel, Lenz, Christof, Urlaub, Henning, Abu-Taha, Issam, Kamler, Markus, Chiang, David Y, Lahiri, Satadru K, Reynolds, Julia O, Quick, Ann P, Scott, Larry, Word, Tarah A, Gelves, Maria D, Heck, Albert J.R, Li, Na, Dobrev, Dobromir, Lehnart, Stephan E, Wehrens, Xander H.T
Published in Circulation (New York, N.Y.) (20.08.2019)
Published in Circulation (New York, N.Y.) (20.08.2019)
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Journal Article
Calmodulin kinase II regulates atrial myocyte late sodium current, calcium handling, and atrial arrhythmia
Greer-Short, Amara, Musa, Hassan, Alsina, Katherina M., Ni, Li, Word, Tarah A., Reynolds, Julia O., Gratz, Daniel, Lane, Cemantha, El-Refaey, Mona, Unudurthi, Sathya, Skaf, Michel, Li, Ning, Fedorov, Vadim V., Wehrens, Xander H.T., Mohler, Peter J., Hund, Thomas J.
Published in Heart rhythm (01.03.2020)
Published in Heart rhythm (01.03.2020)
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Journal Article
Efficacy of RyR2 inhibitor EL20 in induced pluripotent stem cell-derived cardiomyocytes from a patient with catecholaminergic polymorphic ventricular tachycardia
Word, Tarah A, Quick, Ann P, Miyake, Christina Y, Shak, Mayra K, Pan, Xiaolu, Kim, Jean J, Allen, Hugh D, Sibrian-Vazquez, Martha, Strongin, Robert M, Landstrom, Andrew P, Wehrens, Xander H T
Published in Journal of cellular and molecular medicine (01.07.2021)
Published in Journal of cellular and molecular medicine (01.07.2021)
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Journal Article
Nonsense Variant PRDM16-Q187X Causes Impaired Myocardial Development and TGF-β Signaling Resulting in Noncompaction Cardiomyopathy in Humans and Mice
Sun, Bo, Rouzbehani, Omid M T, Kramer, Ryan J, Ghosh, Rajeshwary, Perelli, Robin M, Atkins, Sage, Fatahian, Amir Nima, Davis, Kathryn, Szulik, Marta W, Goodman, Michael A, Hathaway, Marissa A, Chi, Ellenor, Word, Tarah A, Tunuguntla, Hari, Denfield, Susan W, Wehrens, Xander H T, Whitehead, Kevin J, Abdelnasser, Hala Y, Warren, Junco S, Wu, Mingfu, Franklin, Sarah, Boudina, Sihem, Landstrom, Andrew P
Published in Circulation. Heart failure (01.12.2023)
Published in Circulation. Heart failure (01.12.2023)
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Journal Article
Reduction in Junctophilin 2 Expression in Cardiac Nodal Tissue Results in Intracellular Calcium-Driven Increase in Nodal Cell Automaticity
Landstrom, Andrew P, Yang, Qixin, Sun, Bo, Perelli, Robin M, Bidzimou, Minu-Tshyeto, Zhang, Zhushan, Aguilar-Sanchez, Yuriana, Alsina, Katherina M, Cao, Shuyi, Reynolds, Julia O, Word, Tarah A, van der Sangen, Niels M R, Wells, Quinn, Kannankeril, Prince J, Ludwig, Andreas, Kim, Jeffrey J, Wehrens, Xander H T
Published in Circulation. Arrhythmia and electrophysiology (01.02.2023)
Published in Circulation. Arrhythmia and electrophysiology (01.02.2023)
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Journal Article
Removal of pain-relieving drugs from aqueous solutions using Octolig and selected metalloligs
Martin, Dean F., Sehgal, Tanya, Word, Tarah A.
Published in Journal of environmental science and health. Part A, Toxic/hazardous substances & environmental engineering (03.07.2015)
Published in Journal of environmental science and health. Part A, Toxic/hazardous substances & environmental engineering (03.07.2015)
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Journal Article
Using Photoacoustic Calorimetry to Study the cis- to trans- Photoisomerization of the [Ru(II)(2,2'-bipyridine)2(H2O)2]2+ Complex in Aqueous Solution
Word, Tarah A., Karolak, Aleksandra, Cioce, Christian R., Van Der Vaart, Arjan, Larsen, Randy W.
Published in Comments on modern chemistry. Part A, Comments on inorganic chemistry (01.11.2016)
Published in Comments on modern chemistry. Part A, Comments on inorganic chemistry (01.11.2016)
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Journal Article
Abstract 215: Assessing the Efficacy of Novel RYR2 Inhibitor, EL20, in Induced Pluripotent Stem Cell Derived Cardiomyocytes from a Catecholaminergic Polymorphic Ventricular Tachycardia Patient
Word, Tarah A, Landstrom, Andrew, Quick, Ann, Shak, Mayra, Miyake, Christina, Allen, Hugh D, Wehrens, Xander
Published in Circulation research (02.08.2019)
Published in Circulation research (02.08.2019)
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Journal Article
Loss of SPEG Inhibitory Phosphorylation of RyR2 Promotes Atrial Fibrillation
Campbell, Hannah M., Quick, Ann P., Abu-Taha, Issam, Chiang, David Y., Kramm, Carlos F., Word, Tarah A., Brandenburg, Sören, Hulsurkar, Mohit, Alsina, Katherina M., Liu, Hui-Bin, Martin, Brian, Uhlenkamp, Dennis, Moore, Oliver M., Lahiri, Satadru K., Corradini, Eleonora, Kamler, Markus, Heck, Albert J.R., Lehnart, Stephan E., Dobrev, Dobromir, Wehrens, Xander H.T.
Published in Circulation (New York, N.Y.) (20.07.2020)
Published in Circulation (New York, N.Y.) (20.07.2020)
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Journal Article
In Vivo Ryr 2 Editing Corrects Catecholaminergic Polymorphic Ventricular Tachycardia
Pan, Xiaolu, Philippen, Leonne, Lahiri, Satadru K., Lee, Ciaran, Park, So Hyun, Word, Tarah A., Li, Na, Jarrett, Kelsey E., Gupta, Rajat, Reynolds, Julia O., Lin, Jean, Bao, Gang, Lagor, William R., Wehrens, Xander H.T.
Published in Circulation research (28.09.2018)
Published in Circulation research (28.09.2018)
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Journal Article