Mitochondrial complex I inhibition triggers a mitophagy-dependent ROS increase leading to necroptosis and ferroptosis in melanoma cells
Basit, Farhan, van Oppen, Lisanne Mpe, Schöckel, Laura, Bossenbroek, Hasse M, van Emst-de Vries, Sjenet E, Hermeling, Johannes Cw, Grefte, Sander, Kopitz, Charlotte, Heroult, Melanie, Hgm Willems, Peter, Koopman, Werner Jh
Published in Cell death & disease (30.03.2017)
Published in Cell death & disease (30.03.2017)
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Mitochondrial disorders in children: toward development of small‐molecule treatment strategies
Koopman, Werner JH, Beyrath, Julien, Fung, Cheuk‐Wing, Koene, Saskia, Rodenburg, Richard J, Willems, Peter HGM, Smeitink, Jan AM
Published in EMBO molecular medicine (01.04.2016)
Published in EMBO molecular medicine (01.04.2016)
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Journal Article
Targeting mitochondrial complex I using BAY 87-2243 reduces melanoma tumor growth
Schöckel, Laura, Glasauer, Andrea, Basit, Farhan, Bitschar, Katharina, Truong, Hoa, Erdmann, Gerrit, Algire, Carolyn, Hägebarth, Andrea, Willems, Peter Hgm, Kopitz, Charlotte, Koopman, Werner Jh, Héroult, Mélanie
Published in Cancer & metabolism (20.10.2015)
Published in Cancer & metabolism (20.10.2015)
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Journal Article
Monogenic Mitochondrial Disorders
Koopman, Werner J.H, Willems, Peter H.G.M, Smeitink, Jan A.M
Published in The New England journal of medicine (22.03.2012)
Published in The New England journal of medicine (22.03.2012)
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Journal Article
Mitochondrial Morphofunction in Mammalian Cells
Bulthuis, Elianne P, Adjobo-Hermans, Merel J W, Willems, Peter H G M, Koopman, Werner J H
Published in Antioxidants & redox signaling (20.06.2019)
Published in Antioxidants & redox signaling (20.06.2019)
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Journal Article
OXPHOS mutations and neurodegeneration
Koopman, Werner J H, Distelmaier, Felix, Smeitink, Jan AM, Willems, Peter HGM
Published in The EMBO journal (09.01.2013)
Published in The EMBO journal (09.01.2013)
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Journal Article
Depletion of PINK1 affects mitochondrial metabolism, calcium homeostasis and energy maintenance
Heeman, Bavo, Van den Haute, Chris, Aelvoet, Sarah-Ann, Valsecchi, Federica, Rodenburg, Richard J, Reumers, Veerle, Debyser, Zeger, Callewaert, Geert, Koopman, Werner J H, Willems, Peter H G M, Baekelandt, Veerle
Published in Journal of cell science (01.04.2011)
Published in Journal of cell science (01.04.2011)
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Journal Article
Mitochondrial complex I deficiency: from organelle dysfunction to clinical disease
Distelmaier, Felix, Koopman, Werner J.H., van den Heuvel, Lambertus P., Rodenburg, Richard J., Mayatepek, Ertan, Willems, Peter H.G.M., Smeitink, Jan A.M.
Published in Brain (London, England : 1878) (01.04.2009)
Published in Brain (London, England : 1878) (01.04.2009)
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A mutation in the FAM36A gene, the human ortholog of COX20, impairs cytochrome c oxidase assembly and is associated with ataxia and muscle hypotonia
Szklarczyk, Radek, Wanschers, Bas F J, Nijtmans, Leo G, Rodenburg, Richard J, Zschocke, Johannes, Dikow, Nicola, van den Brand, Mariël A M, Hendriks-Franssen, Marthe G M, Gilissen, Christian, Veltman, Joris A, Nooteboom, Marco, Koopman, Werner J H, Willems, Peter H G M, Smeitink, Jan A M, Huynen, Martijn A, van den Heuvel, Lambertus P
Published in Human molecular genetics (15.02.2013)
Published in Human molecular genetics (15.02.2013)
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Journal Article
Cytosolic signaling protein Ecsit also localizes to mitochondria where it interacts with chaperone NDUFAF1 and functions in complex I assembly
Vogel, Rutger O, Janssen, Rolf J R J, van den Brand, Mariël A M, Dieteren, Cindy E J, Verkaart, Sjoerd, Koopman, Werner J H, Willems, Peter H G M, Pluk, Wendy, van den Heuvel, Lambert P W J, Smeitink, Jan A M, Nijtmans, Leo G J
Published in Genes & development (01.03.2007)
Published in Genes & development (01.03.2007)
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Journal Article
Functional Analysis of Picornavirus 2B Proteins: Effects on Calcium Homeostasis and Intracellular Protein Trafficking
DE JONG, Arjan S, DE MATTIA, Fabrizio, VAN DOMMELEN, Michiel M, LANKE, Kjerstin, MELCHERS, Willem J. G, WILLEMS, Peter H. G. M, VAN KUPPEVELD, Frank J. M
Published in Journal of Virology (01.04.2008)
Published in Journal of Virology (01.04.2008)
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Journal Article
The antioxidant Trolox restores mitochondrial membrane potential and Ca2+-stimulated ATP production in human complex I deficiency
Distelmaier, Felix, Visch, Henk-Jan, Smeitink, Jan A. M., Mayatepek, Ertan, Koopman, Werner J. H., Willems, Peter H. G. M.
Published in Journal of molecular medicine (Berlin, Germany) (01.05.2009)
Published in Journal of molecular medicine (Berlin, Germany) (01.05.2009)
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Journal Article
Mitochondrial processes are impaired in hereditary inclusion body myopathy
Eisenberg, Iris, Novershtern, Noa, Itzhaki, Zohar, Becker-Cohen, Michal, Sadeh, Menachem, Willems, Peter H.G.M., Friedman, Nir, Koopman, Werner J.H., Mitrani-Rosenbaum, Stella
Published in Human molecular genetics (01.12.2008)
Published in Human molecular genetics (01.12.2008)
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Journal Article
Activated leukocyte cell adhesion molecule (ALCAM/CD166/MEMD), a novel actor in invasive growth, controls matrix metalloproteinase activity
LUNTER, Pim C, VAN KILSDONK, Jeroen W. J, VAN BECK, Hanneke, CORNELISSEN, Ine M. H. A, BERGERS, Mieke, WILLEMS, Peter H. G. M, VAN MUIJEN, Goos N. P, SWART, Guido W. M
Published in Cancer research (Chicago, Ill.) (01.10.2005)
Published in Cancer research (Chicago, Ill.) (01.10.2005)
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