B cell subsets in healthy children: Reference values for evaluation of B cell maturation process in peripheral blood
Piątosa, Barbara, Wolska‐Kuśnierz, Beata, Pac, Małgorzata, Siewiera, Katarzyna, Gałkowska, Ewa, Bernatowska, Ewa
Published in Cytometry. Part B, Clinical cytometry (01.11.2010)
Published in Cytometry. Part B, Clinical cytometry (01.11.2010)
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T Lymphocytes in Patients With Nijmegen Breakage Syndrome Demonstrate Features of Exhaustion and Senescence in Flow Cytometric Evaluation of Maturation Pathway
Piatosa, Barbara, Wolska-Kuśnierz, Beata, Tkaczyk, Katarzyna, Heropolitanska-Pliszka, Edyta, Grycuk, Urszula, Wakulinska, Anna, Gregorek, Hanna
Published in Frontiers in immunology (30.06.2020)
Published in Frontiers in immunology (30.06.2020)
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National experience with adenosine deaminase deficiency related SCID in Polish children
Dąbrowska-Leonik, Nel, Piątosa, Barbara, Słomińska, Ewa, Bohynikova, Nadezda, Bernat-Sitarz, Katarzyna, Bernatowska, Ewa, Wolska-Kuśnierz, Beata, Kałwak, Krzysztof, Kołtan, Sylwia, Dąbrowska, Anna, Goździk, Jolanta, Ussowicz, Marek, Pac, Małgorzata
Published in Frontiers in immunology (06.01.2023)
Published in Frontiers in immunology (06.01.2023)
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Progressive Bronchiectasis and CMC in a Patient with STAT1 GOF—A Rare Case of Primary Immunodeficiency
Dmeńska, Hanna, Pac, Małgorzata, Skomska-Pawliszak, Małgorzata, Pietrucha, Barbara, Wolska-Kuśnierz, Beata, Piątosa, Barbara, Komarnicka, Justyna, Heropolitańska-Pliszka, Edyta
Published in Advances in respiratory medicine (01.01.2020)
Published in Advances in respiratory medicine (01.01.2020)
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Common Variable Immune Deficiency in Children—Clinical Characteristics Varies Depending on Defect in Peripheral B Cell Maturation
Piątosa, Barbara, Pac, Małgorzata, Siewiera, Katarzyna, Pietrucha, Barbara, Klaudel-Dreszler, Maja, Heropolitańska-Pliszka, Edyta, Wolska-Kuśnierz, Beata, Dmeńska, Hanna, Gregorek, Hanna, Sokolnicka, Irena, Rękawek, Aneta, Tkaczyk, Katarzyna, Bernatowska, Ewa
Published in Journal of clinical immunology (01.05.2013)
Published in Journal of clinical immunology (01.05.2013)
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Inheritance of STING mosaicism in two half-siblings
de Becdelièvre, Alix, Eveillard, Laurye-Anne, Wolska-Kuśnierz, Beata, Frémond, Marie-Louise
Published in Journal of clinical immunology (01.10.2024)
Published in Journal of clinical immunology (01.10.2024)
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Prevalence of Cryptosporidium, Blastocystis, and other opportunistic infections in patients with primary and acquired immunodeficiency
Bednarska, Małgorzata, Jankowska, Irena, Pawelas, Andrzej, Piwczyńska, Karolina, Bajer, Anna, Wolska-Kuśnierz, Beata, Wielopolska, Małgorzata, Welc-Falęciak, Renata
Published in Parasitology research (1987) (01.09.2018)
Published in Parasitology research (1987) (01.09.2018)
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Periodic fever syndromes in Eastern and Central European countries: results of a pediatric multinational survey
Toplak, Nataša, Dolezalovà, Pavla, Constantin, Tamas, Sedivà, Anna, Pašić, Srdjan, Cižnar, Peter, Wolska-Kuśnierz, Beata, Harjaček, Miroslav, Stefan, Mariana, Ruperto, Nicolino, Gattorno, Marco, Avčin, Tadej
Published in Pediatric Rheumatology (02.12.2010)
Published in Pediatric Rheumatology (02.12.2010)
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Treosulfan-based conditioning regimen in a second matched unrelated peripheral blood stem cell transplantation for a pediatric patient with CGD and invasive aspergillosis, who experienced initial graft failure after RIC
Klaudel-Dreszler, Maja Agnieszka, Kalwak, Krzysztof, Kurenko-Deptuch, Magdalena, Wolska-Kusnierz, Beata, Heropolitanska-Pliszka, Edyta, Pietrucha, Barbara, Mikoluc, Bożena, Gorczyńska, Ewa, Ussowicz, Marek, Chybicka, Alicja, Bernatowska, Ewa
Published in International journal of hematology (01.12.2009)
Published in International journal of hematology (01.12.2009)
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Antioxidant Defense, Redox Homeostasis, and Oxidative Damage in Children With Ataxia Telangiectasia and Nijmegen Breakage Syndrome
Maciejczyk, Mateusz, Heropolitanska-Pliszka, Edyta, Pietrucha, Barbara, Sawicka-Powierza, Jolanta, Bernatowska, Ewa, Wolska-Kusnierz, Beata, Pac, Małgorzata, Car, Halina, Zalewska, Anna, Mikoluc, Bozena
Published in Frontiers in immunology (27.09.2019)
Published in Frontiers in immunology (27.09.2019)
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Human CD19 and CD40L deficiencies impair antibody selection and differentially affect somatic hypermutation
van Zelm, Menno C., PhD, Bartol, Sophinus J.W., BSc, Driessen, Gertjan J., MD, PhD, Mascart, Françoise, MD, PhD, Reisli, Ismail, MD, Franco, Jose L., MD, Wolska-Kusnierz, Beata, MD, Kanegane, Hirokazu, MD, PhD, Boon, Louis, PhD, van Dongen, Jacques J.M., MD, PhD, van der Burg, Mirjam, PhD
Published in Journal of allergy and clinical immunology (01.07.2014)
Published in Journal of allergy and clinical immunology (01.07.2014)
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Combined liver and hematopoietic stem cell transplantation in patients with X-linked hyper-IgM syndrome
Bucciol, Giorgia, Nicholas, Sarah K., Calvo, Pier Luigi, Cant, Andrew, Edgar, J. David M., Español, Teresa, Ferrua, Francesca, Galicchio, Miguel, Gennery, Andrew R., Hadzic, Nedim, Hanson, I. Celine, Kusminsky, Gustavo, Lange, Andrzej, Lanternier, Fanny, Mahlaoui, Nizar, Moshous, Despina, Nademi, Zohreh, Neven, Benedicte, Oleastro, Matias, Porta, Fulvio, Quarello, Paola, Silva, Marcelo, Slatter, Mary A., Soncini, Elena, Stefanowicz, Marek, Tandoi, Francesco, Teisseyre, Mikołaj, Torgerson, Troy R., Veys, Paul, Weinacht, Katja G., Wolska-Kuśnierz, Beata, Pirenne, Jacques, de la Morena, M. Teresa, Meyts, Isabelle
Published in Journal of allergy and clinical immunology (01.05.2019)
Published in Journal of allergy and clinical immunology (01.05.2019)
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Similar recombination-activating gene ( RAG ) mutations result in similar immunobiological effects but in different clinical phenotypes
IJspeert, Hanna, MSc, Driessen, Gertjan J., MD, PhD, Moorhouse, Michael J., PhD, Hartwig, Nico G., MD, PhD, Wolska-Kusnierz, Beata, MD, Kalwak, Krzysztof, MD, Pituch-Noworolska, Anna, MD, Kondratenko, Irina, MD, van Montfrans, Joris M., MD, PhD, Mejstrikova, Ester, MD, Lankester, Arjan C., MD, PhD, Langerak, Anton W., PhD, van Gent, Dik C., PhD, Stubbs, Andrew P., PhD, van Dongen, Jacques J.M., MD, PhD, van der Burg, Mirjam, PhD
Published in Journal of allergy and clinical immunology (01.04.2014)
Published in Journal of allergy and clinical immunology (01.04.2014)
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Successful Allogeneic Stem Cell Transplantation in Nuclear Factor-Kappa B Essential Modulator Deficiency Syndrome After Treosulfan-Based Conditioning: A Case Report
Martuszewski, Adrian, Paluszkiewicz, Patrycja, Sierżęga-Staykov, Katarzyna, Wawrzyniak-Dzierżek, Elżbieta, Salamonowicz-Bodzioch, Małgorzata, Frączkiewicz, Jowita, Janeczko-Czarnecka, Małgorzata, Mielcarek-Siedziuk, Monika, Nowak, Mateusz, Dąbrowska-Leonik, Nel, Wolska-Kuśnierz, Beata, Gul, Katarzyna, Bąbol-Pokora, Katarzyna, Młynarski, Wojciech, Kałwak, Krzysztof, Ussowicz, Marek
Published in Transplantation proceedings (01.03.2020)
Published in Transplantation proceedings (01.03.2020)
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COVID-19 in unvaccinated patients with inborn errors of immunity—polish experience
Kołtan, Sylwia, Ziętkiewicz, Marcin, Grześk, Elżbieta, Becht, Rafał, Berdej-Szczot, Elżbieta, Cienkusz, Magdalena, Ewertowska, Marlena, Heropolitańska-Pliszka, Edyta, Krysiak, Natalia, Lewandowicz-Uszyńska, Aleksandra, Mach-Tomalska, Monika, Matyja-Bednarczyk, Aleksandra, Milchert, Marcin, Napiórkowska-Baran, Katarzyna, Pieniawska-Śmiech, Karolina, Pituch-Noworolska, Anna, Renke, Joanna, Roliński, Jacek, Rywczak, Iwona, Stelmach-Gołdyś, Agnieszka, Strach, Magdalena, Suchanek, Hanna, Sulicka-Grodzicka, Joanna, Szczawińska-Popłonyk, Aleksandra, Tokarski, Sławomir, Więsik-Szewczyk, Ewa, Wolska-Kuśnierz, Beata, Zeman, Krzysztof, Pac, Małgorzata
Published in Frontiers in immunology (23.09.2022)
Published in Frontiers in immunology (23.09.2022)
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BCG Moreau Vaccine Safety Profile and NK Cells—Double Protection Against Disseminated BCG Infection in Retrospective Study of BCG Vaccination in 52 Polish Children with Severe Combined Immunodeficiency
Bernatowska, Ewa, Skomska-Pawliszak, Małgorzta, Wolska-Kuśnierz, Beata, Pac, Małgorzata, Heropolitanska-Pliszka, Edyta, Pietrucha, Barbara, Bernat-Sitarz, Katarzyna, Dąbrowska-Leonik, Nel, Bohynikova, Nadia, Piątosa, Barbara, Lutyńska, Anna, Augustynowicz, Ewa, Augustynowicz-Kopeć, Ewa, Korzeniewska-Koseła, Maria, Krasińska, Maria, Krzysztopa-Grzybowska, Katarzyna, Wieteska-Klimczak, Anna, Książyk, Janusz, Jackowska, Teresa, van den Burg, Mirjam, van Dongen, Jacques J. M., Casanova, Jean-Laurent, Picard, Capucine, Mikołuć, Bożena
Published in Journal of clinical immunology (01.01.2020)
Published in Journal of clinical immunology (01.01.2020)
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EuroFlow Standardized Approach to Diagnostic Immunopheneotyping of Severe PID in Newborns and Young Children
Kalina, Tomas, Bakardjieva, Marina, Blom, Maartje, Perez-Andres, Martin, Barendregt, Barbara, Kanderová, Veronika, Bonroy, Carolien, Philippé, Jan, Blanco, Elena, Pico-Knijnenburg, Ingrid, Paping, Jitse H M P, Wolska-Kuśnierz, Beata, Pac, Malgorzata, Tkazcyk, Jakub, Haerynck, Filomeen, Akar, Himmet Haluk, Formánková, Renata, Freiberger, Tomáš, Svatoň, Michael, Šedivá, Anna, Arriba-Méndez, Sonia, Orfao, Alberto, van Dongen, Jacques J M, van der Burg, Mirjam
Published in Frontiers in immunology (19.03.2020)
Published in Frontiers in immunology (19.03.2020)
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Vitamin D deficiency in children with recurrent respiratory infections, with or without immunoglobulin deficiency
Dąbrowska-Leonik, Nel, Bernatowska, Ewa, Pac, Małgorzata, Filipiuk, Wiktor, Mulawka, Jan, Pietrucha, Barbara, Heropolitańska-Pliszka, Edyta, Bernat-Sitarz, Katarzyna, Wolska-Kuśnierz, Beata, Mikołuć, Bożena
Published in Advances in medical sciences (01.03.2018)
Published in Advances in medical sciences (01.03.2018)
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Systemic Redox Imbalance in Patients with Chronic Granulomatous Disease
Heropolitanska-Pliszka, Edyta, Berk, Klaudia, Maciejczyk, Mateusz, Sawicka-Powierza, Jolanta, Bernatowska, Ewa, Wolska-Kusnierz, Beata, Pac, Malgorzata, Dabrowska-Leonik, Nel, Piatosa, Barbara, Lewandowicz-Uszynska, Aleksandra, Karpinska, Joanna, Zalewska, Anna, Mikoluc, Bozena
Published in Journal of clinical medicine (09.05.2020)
Published in Journal of clinical medicine (09.05.2020)
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