Mechanistic Bases of Neurotoxicity Provoked by Fatty Acids Accumulating in MCAD and LCHAD Deficiencies
Amaral, Alexandre U., Cecatto, Cristiane, da Silva, Janaína C., Wajner, Alessandro, Wajner, Moacir
Published in Journal of Inborn Errors of Metabolism and Screening (2017)
Published in Journal of Inborn Errors of Metabolism and Screening (2017)
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Book Review
Journal Article
Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats
Roginski, Ana Cristina, Wajner, Alessandro, Cecatto, Cristiane, Wajner, Simone Magagnin, Castilho, Roger Frigério, Wajner, Moacir, Amaral, Alexandre Umpierrez
Published in Biochimica et biophysica acta. Molecular basis of disease (01.05.2020)
Published in Biochimica et biophysica acta. Molecular basis of disease (01.05.2020)
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Journal Article
Disturbance of mitochondrial functions associated with permeability transition pore opening induced by cis-5-tetradecenoic and myristic acids in liver of adolescent rats
Cecatto, Cristiane, Amaral, Alexandre Umpierrez, Wajner, Alessandro, Wajner, Simone Magagnin, Castilho, Roger Frigério, Wajner, Moacir
Published in Mitochondrion (01.01.2020)
Published in Mitochondrion (01.01.2020)
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Journal Article
cis-4-Decenoic and decanoic acids impair mitochondrial energy, redox and Ca(2+) homeostasis and induce mitochondrial permeability transition pore opening in rat brain and liver: Possible implications for the pathogenesis of MCAD deficiency
Amaral, Alexandre Umpierrez, Cecatto, Cristiane, da Silva, Janaína Camacho, Wajner, Alessandro, Godoy, Kálita Dos Santos, Ribeiro, Rafael Teixeira, Wajner, Moacir
Published in Biochimica et biophysica acta (01.09.2016)
Published in Biochimica et biophysica acta (01.09.2016)
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Journal Article
High vulnerability of the heart and liver to 3‐hydroxypalmitic acid–induced disruption of mitochondrial functions in intact cell systems
Cecatto, Cristiane, Wajner, Alessandro, Vargas, Carmen Regla, Wajner, Simone Magagnin, Amaral, Alexandre Umpierrez, Wajner, Moacir
Published in Journal of cellular biochemistry (01.09.2018)
Published in Journal of cellular biochemistry (01.09.2018)
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Journal Article
cis-4-Decenoic and decanoic acids impair mitochondrial energy, redox and Ca2+ homeostasis and induce mitochondrial permeability transition pore opening in rat brain and liver: Possible implications for the pathogenesis of MCAD deficiency
Amaral, Alexandre Umpierrez, Cecatto, Cristiane, da Silva, Janaína Camacho, Wajner, Alessandro, Godoy, Kálita dos Santos, Ribeiro, Rafael Teixeira, Wajner, Moacir
Published in Biochimica et biophysica acta. Bioenergetics (01.09.2016)
Published in Biochimica et biophysica acta. Bioenergetics (01.09.2016)
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Journal Article
Metabolite accumulation in VLCAD deficiency markedly disrupts mitochondrial bioenergetics and Ca2+ homeostasis in the heart
Cecatto, Cristiane, Amaral, Alexandre Umpierrez, Silva, Janaína Camacho, Wajner, Alessandro, Schimit, Mariana de Oliveira Vargas, Silva, Lucas Henrique Rodrigues, Wajner, Simone Magagnin, Zanatta, Ângela, Castilho, Roger Frigério, Wajner, Moacir
Published in The FEBS journal (01.04.2018)
Published in The FEBS journal (01.04.2018)
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Journal Article
cis-4-Decenoic and decanoic acids impair mitochondrial energy, redox and Ca 2+ homeostasis and induce mitochondrial permeability transition pore opening in rat brain and liver: Possible implications for the pathogenesis of MCAD deficiency
Amaral, Alexandre Umpierrez, Cecatto, Cristiane, da Silva, Janaína Camacho, Wajner, Alessandro, Godoy, Kálita dos Santos, Ribeiro, Rafael Teixeira, Wajner, Moacir
Published in Biochimica et biophysica acta. Bioenergetics (01.09.2016)
Published in Biochimica et biophysica acta. Bioenergetics (01.09.2016)
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Journal Article
Metabolite accumulation in VLCAD deficiency markedly disrupts mitochondrial bioenergetics and Ca 2+ homeostasis in the heart
Cecatto, Cristiane, Amaral, Alexandre Umpierrez, da Silva, Janaína Camacho, Wajner, Alessandro, Schimit, Mariana de Oliveira Vargas, da Silva, Lucas Henrique Rodrigues, Wajner, Simone Magagnin, Zanatta, Ângela, Castilho, Roger Frigério, Wajner, Moacir
Published in The FEBS journal (01.04.2018)
Published in The FEBS journal (01.04.2018)
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Journal Article
Mevalonolactone disrupts mitochondrial functions and induces permeability transition pore opening in rat brain mitochondria: Implications for the pathogenesis of mevalonic aciduria
Cecatto, Cristiane, Amaral, Alexandre Umpierrez, da Silva, Janaína Camacho, Wajner, Alessandro, Godoy, Kálita dos Santos, Ribeiro, Rafael Teixeira, Gonçalves, Aline de Mello, Vargas, Carmen Regla, Wajner, Moacir
Published in Neurochemistry international (01.09.2017)
Published in Neurochemistry international (01.09.2017)
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Journal Article
α-Ketoadipic Acid and α-Aminoadipic Acid Cause Disturbance of Glutamatergic Neurotransmission and Induction of Oxidative Stress In Vitro in Brain of Adolescent Rats
da Silva, Janaína Camacho, Amaral, Alexandre Umpierrez, Cecatto, Cristiane, Wajner, Alessandro, dos Santos Godoy, Kálita, Ribeiro, Rafael Teixeira, de Mello Gonçalves, Aline, Zanatta, Ângela, da Rosa, Mateus Struecker, Loureiro, Samanta Oliveira, Vargas, Carmen Regla, Leipnitz, Guilhian, de Souza, Diogo Onofre Gomes, Wajner, Moacir
Published in Neurotoxicity research (01.08.2017)
Published in Neurotoxicity research (01.08.2017)
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Journal Article
Biochemical characterization of chitotriosidase enzyme: comparison between normal individuals and patients with Gaucher and with Niemann–Pick diseases
Wajner, Alessandro, Michelin, Kristiane, Burin, Maira G., Pires, Ricardo F., Pereira, Maria Luiza S., Giugliani, Roberto, Coelho, Janice C.
Published in Clinical biochemistry (01.10.2004)
Published in Clinical biochemistry (01.10.2004)
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Journal Article
Comparison between the biochemical properties of plasma chitotriosidase from normal individuals and from patients with Gaucher disease, GM1-gangliosidosis, Krabbe disease and heterozygotes for Gaucher disease
Wajner, Alessandro, Michelin, Kristiane, Burin, Maira G., Pires, Ricardo F., Pereira, Maria Luiza S., Giugliani, Roberto, Coelho, Janice C.
Published in Clinical biochemistry (01.03.2007)
Published in Clinical biochemistry (01.03.2007)
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Journal Article
Biochemical properties of β-glucosidase in leukocytes from patients and obligated heterozygotes for Gaucher disease carriers
Michelin, Kristiane, Wajner, Alessandro, Bock, Hugo, Fachel, Ângela, Rosenberg, Roberto, Flores Pires, Ricardo, Saraiva Pereira, Maria Luiza, Giugliani, Roberto, Coelho, Janice Carneiro
Published in Clinica chimica acta (01.12.2005)
Published in Clinica chimica acta (01.12.2005)
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Journal Article
Biochemical study on β-glucosidase in individuals with Gaucher's disease and normal subjects
Michelin, Kristiane, Wajner, Alessandro, Goulart, Laureci da S., Fachel, Ângela A., Pereira, Maria Luiza S., de Mello, Alexandre S., Souza, Fernanda T.S., Pires, Ricardo F., Giugliani, Roberto, Coelho, Janice C.
Published in Clinica chimica acta (01.05.2004)
Published in Clinica chimica acta (01.05.2004)
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Journal Article
Application of a comprehensive protocol for the identification of Gaucher disease in Brazil
Michelin, Kristiane, Wajner, Alessandro, de Souza, Fernanda T.S., de Mello, Alexandre S., Burin, Maira G., Pereira, Maria Luiza S., Pires, Ricardo F., Giugliani, Roberto, Coelho, Janice C.
Published in American journal of medical genetics. Part A (01.07.2005)
Published in American journal of medical genetics. Part A (01.07.2005)
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Journal Article