ALS/FTD-Linked Mutation in FUS Suppresses Intra-axonal Protein Synthesis and Drives Disease Without Nuclear Loss-of-Function of FUS
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Published in Neuron (Cambridge, Mass.) (21.11.2018)
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Enhancing mitochondrial calcium buffering capacity reduces aggregation of misfolded SOD1 and motor neuron cell death without extending survival in mouse models of inherited amyotrophic lateral sclerosis
Parone, Philippe A, Da Cruz, Sandrine, Han, Joo Seok, McAlonis-Downes, Melissa, Vetto, Anne P, Lee, Sandra K, Tseng, Eva, Cleveland, Don W
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Published in The Journal of neuroscience (13.03.2013)
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Elevated PGC-1α Activity Sustains Mitochondrial Biogenesis and Muscle Function without Extending Survival in a Mouse Model of Inherited ALS
Da Cruz, Sandrine, Parone, Philippe A., Lopes, Vanda S., Lillo, Concepción, McAlonis-Downes, Melissa, Lee, Sandra K., Vetto, Anne P., Petrosyan, Susanna, Marsala, Martin, Murphy, Anne N., Williams, David S., Spiegelman, Bruce M., Cleveland, Don W.
Published in Cell metabolism (02.05.2012)
Published in Cell metabolism (02.05.2012)
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Overriding FUS autoregulation in mice triggers gain-of-toxic dysfunctions in RNA metabolism and autophagy-lysosome axis
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Published in eLife (12.02.2019)
Published in eLife (12.02.2019)
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Journal Article
ALS/FTD-Linked Mutation in FUS Suppresses Intra-axonal Protein Synthesis and Drives Disease Without Nuclear Loss-of-Function of FUS
López-Erauskin, Jone, Tadokoro, Takahiro, Baughn, Michael W., Myers, Brian, McAlonis-Downes, Melissa, Chillon-Marinas, Carlos, Asiaban, Joshua N., Artates, Jonathan, Bui, Anh T., Vetto, Anne P., Lee, Sandra K., Le, Ai Vy, Sun, Ying, Jambeau, Mélanie, Boubaker, Jihane, Swing, Deborah, Qiu, Jinsong, Hicks, Geoffrey G., Ouyang, Zhengyu, Fu, Xiang-Dong, Tessarollo, Lino, Ling, Shuo-Chien, Parone, Philippe A., Shaw, Christopher E., Marsala, Martin, Lagier-Tourenne, Clotilde, Cleveland, Don W., Da Cruz, Sandrine
Published in Neuron (Cambridge, Mass.) (22.04.2020)
Published in Neuron (Cambridge, Mass.) (22.04.2020)
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Reproducibility Needs Reshape Scientific Data Governance
Meijer, Paul, Aggoune, Yousef, Ambrose, Madeline, Beaubien, Aldan, Harvey, James, Howard, Nicole, Inala, Neelima, Johnson, Ed, Kelsey, Autumn, Kinsey, Melissa, Liang, Jessica, Mariz, Paul, Pister, Stark, Subramanian, Sathya, Tereshchenko, Vitalii, Vetto, Anne
Year of Publication 29.09.2024
Year of Publication 29.09.2024
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Provide Proactive Reproducible Analysis Transparency with Every Publication
Meijer, Paul, Howard, Nicole, Liang, Jessica, Kelsey, Autumn, Subramanian, Sathya, Johnson, Ed, Mariz, Paul, Harvey, James, Ambrose, Madeline, Tereshchenko, Vitalii, Beaubien, Aldan, Inala, Neelima, Aggoune, Yousef, Pister, Stark, Vetto, Anne, Kinsey, Melissa, Bumol, Tom, Goldrath, Ananda, Li, Xiaojun, Torgerson, Troy, Skene, Peter, Okada, Lauren, La France, Christian, Thomson, Zach, Graybuck, Lucas
Year of Publication 17.08.2024
Year of Publication 17.08.2024
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Journal Article
Reproducibility Needs Reshape Scientific Data Governance
Meijer, Paul, Aggoune, Yousef, Ambrose, Madeline, Beaubien, Aldan, Harvey, James, Howard, Nicole, Inala, Neelima, Johnson, Ed, Kelsey, Autumn, Kinsey, Melissa, Liang, Jessica, Mariz, Paul, Stark Pister, Subramanian, Sathya, Tereshchenko, Vitalii, Vetto, Anne
Published in arXiv.org (29.09.2024)
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Published in arXiv.org (29.09.2024)
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Provide Proactive Reproducible Analysis Transparency with Every Publication
Meijer, Paul, Howard, Nicole, Liang, Jessica, Kelsey, Autumn, Subramanian, Sathya, Johnson, Ed, Mariz, Paul, Harvey, James, Ambrose, Madeline, Tereshchenko, Vitalii, Beaubien, Aldan, Inala, Neelima, Aggoune, Yousef, Stark Pister, Vetto, Anne, Kinsey, Melissa, Bumol, Tom, Goldrath, Ananda, Li, Xiaojun, Torgerson, Troy, Skene, Peter, Okada, Lauren, Christian La France, Thomson, Zach, Lucas Graybuck
Published in arXiv.org (17.08.2024)
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Published in arXiv.org (17.08.2024)
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