Nanocellulose in green food packaging
Vilarinho, Fernanda, Sanches Silva, Ana, Vaz, M Fátima, Farinha, José Paulo
Published in Critical reviews in food science and nutrition (13.06.2018)
Published in Critical reviews in food science and nutrition (13.06.2018)
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Journal Article
Acylcarnitines: reflecting or inflicting insulin resistance?
Schooneman, Marieke G, Vaz, Frédéric M, Houten, Sander M, Soeters, Maarten R
Published in Diabetes (New York, N.Y.) (01.01.2013)
Published in Diabetes (New York, N.Y.) (01.01.2013)
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Journal Article
Modeling the mitochondrial cardiomyopathy of Barth syndrome with induced pluripotent stem cell and heart-on-chip technologies
Wang, Gang, McCain, Megan L, Yang, Luhan, He, Aibin, Pasqualini, Francesco Silvio, Agarwal, Ashutosh, Yuan, Hongyan, Jiang, Dawei, Zhang, Donghui, Zangi, Lior, Geva, Judith, Roberts, Amy E, Ma, Qing, Ding, Jian, Chen, Jinghai, Wang, Da-Zhi, Li, Kai, Wang, Jiwu, Wanders, Ronald J A, Kulik, Wim, Vaz, Frédéric M, Laflamme, Michael A, Murry, Charles E, Chien, Kenneth R, Kelley, Richard I, Church, George M, Parker, Kevin Kit, Pu, William T
Published in Nature medicine (01.06.2014)
Published in Nature medicine (01.06.2014)
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Journal Article
Retrospective study of long-term outcomes of enzyme replacement therapy in Fabry disease: Analysis of prognostic factors
Arends, Maarten, Biegstraaten, Marieke, Hughes, Derralynn A, Mehta, Atul, Elliott, Perry M, Oder, Daniel, Watkinson, Oliver T, Vaz, Frédéric M, van Kuilenburg, André B P, Wanner, Christoph, Hollak, Carla E M
Published in PloS one (01.08.2017)
Published in PloS one (01.08.2017)
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Journal Article
Sodium taurocholate cotransporting polypeptide (SLC10A1) deficiency: Conjugated hypercholanemia without a clear clinical phenotype
Vaz, Frédéric M., Paulusma, Coen C., Huidekoper, Hidde, de Ru, Minke, Lim, Cynthia, Koster, Janet, Ho‐Mok, Kam, Bootsma, Albert H., Groen, Albert K., Schaap, Frank G., Oude Elferink, Ronald P. J., Waterham, Hans R., Wanders, Ronald J.A.
Published in Hepatology (Baltimore, Md.) (01.01.2015)
Published in Hepatology (Baltimore, Md.) (01.01.2015)
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Journal Article
Peroxisomes can oxidize medium- and long-chain fatty acids through a pathway involving ABCD3 and HSD17B4
Violante, Sara, Achetib, Nihad, van Roermund, Carlo W T, Hagen, Jacob, Dodatko, Tetyana, Vaz, Frédéric M, Waterham, Hans R, Chen, Hongjie, Baes, Myriam, Yu, Chunli, Argmann, Carmen A, Houten, Sander M
Published in The FASEB journal (01.03.2019)
Published in The FASEB journal (01.03.2019)
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Journal Article
Active polylactic acid film incorporated with green tea extract: Development, characterization and effectiveness
Martins, Cristiana, Vilarinho, Fernanda, Sanches Silva, Ana, Andrade, Mariana, Machado, Ana V., Castilho, M. Conceição, Sá, Arsénio, Cunha, Américo, Vaz, M. Fátima, Ramos, Fernando
Published in Industrial crops and products (01.11.2018)
Published in Industrial crops and products (01.11.2018)
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Journal Article
Modern viticulture in southern Europe: Vulnerabilities and strategies for adaptation to water scarcity
Costa, J.M., Vaz, M., Escalona, J., Egipto, R., Lopes, C., Medrano, H., Chaves, M.M.
Published in Agricultural water management (31.01.2016)
Published in Agricultural water management (31.01.2016)
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Journal Article
Monitoring lipid oxidation in a processed meat product packaged with nanocomposite poly(lactic acid) film
Vilarinho, Fernanda, Andrade, Mariana, Buonocore, Giovanna G., Stanzione, Mariamelia, Vaz, M. Fátima, Sanches Silva, Ana
Published in European polymer journal (01.01.2018)
Published in European polymer journal (01.01.2018)
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Journal Article
C26:0-Carnitine Is a New Biomarker for X-Linked Adrenoleukodystrophy in Mice and Man
van de Beek, Malu-Clair, Dijkstra, Inge M E, van Lenthe, Henk, Ofman, Rob, Goldhaber-Pasillas, Dalia, Schauer, Nicolas, Schackmann, Martin, Engelen-Lee, Joo-Yeon, Vaz, Frédéric M, Kulik, Wim, Wanders, Ronald J A, Engelen, Marc, Kemp, Stephan
Published in PloS one (28.04.2016)
Published in PloS one (28.04.2016)
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Journal Article
A newborn screening method for cerebrotendinous xanthomatosis using bile alcohol glucuronides and metabolite ratios[S]
Vaz, Frédéric M., Bootsma, Albert H., Kulik, Willem, Verrips, Aad, Wevers, Ron A., Schielen, Peter C., DeBarber, Andrea E., Huidekoper, Hidde H.
Published in Journal of lipid research (01.05.2017)
Published in Journal of lipid research (01.05.2017)
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Journal Article
Pyruvate dehydrogenase complex plays a central role in brown adipocyte energy expenditure and fuel utilization during short-term beta-adrenergic activation
Held, Ntsiki M, Kuipers, Eline N, van Weeghel, Michel, van Klinken, Jan Bert, Denis, Simone W, Lombès, Marc, Wanders, Ronald J, Vaz, Frédéric M, Rensen, Patrick C N, Verhoeven, Arthur J, Boon, Mariëtte R, Houtkooper, Riekelt H
Published in Scientific reports (22.06.2018)
Published in Scientific reports (22.06.2018)
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Journal Article
Agalsidase alfa versus agalsidase beta for the treatment of Fabry disease: an international cohort study
Arends, Maarten, Biegstraaten, Marieke, Wanner, Christoph, Sirrs, Sandra, Mehta, Atul, Elliott, Perry M, Oder, Daniel, Watkinson, Oliver T, Bichet, Daniel G, Khan, Aneal, Iwanochko, Mark, Vaz, Frédéric M, van Kuilenburg, André B P, West, Michael L, Hughes, Derralynn A, Hollak, Carla E M
Published in Journal of medical genetics (01.05.2018)
Published in Journal of medical genetics (01.05.2018)
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