Drosophila CRISPR/Cas9 mutants as tools to analyse cardiac filamin function and pathogenicity of human FLNC variants
Ader, F., Russi, M., Tixier-Cardoso, L., Jullian, E., Martin, E., Richard, P., Villard, E., Monnier, V.
Published in Biology open (01.09.2022)
Published in Biology open (01.09.2022)
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Journal Article
Glial overexpression of Tspo extends lifespan and protects against frataxin deficiency in Drosophila
Jullian, Estelle, Russi, Maria, Turki, Ema, Bouvelot, Margaux, Tixier, Laura, Middendorp, Sandrine, Martin, Elodie, Monnier, Véronique
Published in Biochimie (01.09.2024)
Published in Biochimie (01.09.2024)
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A Drosophila model of Friedreich ataxia with CRISPR/Cas9 insertion of GAA repeats in the frataxin gene reveals in vivo protection by N-acetyl cysteine
Russi, Maria, Martin, Elodie, D’Autréaux, Benoit, Tixier, Laura, Tricoire, Hervé, Monnier, Véronique
Published in Human molecular genetics (10.10.2020)
Published in Human molecular genetics (10.10.2020)
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