Water-Soluble Gd(III)–Porphyrin Complexes Capable of Both Photosensitization and Relaxation Enhancement
Nemeth, Tamas, Yoshizawa-Sugata, Naoko, Pallier, Agnes, Tajima, Youichi, Ma, Yue, Tóth, Éva, Masai, Hisao, Yamakoshi, Yoko
Published in Chemical & biomedical imaging (22.05.2023)
Published in Chemical & biomedical imaging (22.05.2023)
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Journal Article
Depletion of definitive gut endoderm in Sox17-null mutant mice
Kanai-Azuma, Masami, Kanai, Yoshiakira, Gad, Jacqueline M, Tajima, Youichi, Taya, Choji, Kurohmaru, Masamichi, Sanai, Yutaka, Yonekawa, Hiromichi, Yazaki, Kazumori, Tam, Patrick P L, Hayashi, Yoshihiro
Published in Development (Cambridge) (15.05.2002)
Published in Development (Cambridge) (15.05.2002)
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Journal Article
Eukaryotic translation initiation factor 3 (eIF3) subunit e is essential for embryonic development and cell proliferation
Sadato, Daichi, Ono, Tomio, Gotoh‐Saito, Saki, Kajiwara, Naoki, Nomura, Namiko, Ukaji, Masako, Yang, Liying, Sakimura, Kenji, Tajima, Youichi, Oboki, Keisuke, Shibasaki, Futoshi
Published in FEBS open bio (01.08.2018)
Published in FEBS open bio (01.08.2018)
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Journal Article
Residual laminin-binding activity and enhanced dystroglycan glycosylation by LARGE in novel model mice to dystroglycanopathy
Kanagawa, Motoi, Nishimoto, Akemi, Chiyonobu, Tomohiro, Takeda, Satoshi, Miyagoe-Suzuki, Yuko, Wang, Fan, Fujikake, Nobuhiro, Taniguchi, Mariko, Lu, Zhongpeng, Tachikawa, Masaji, Nagai, Yoshitaka, Tashiro, Fumi, Miyazaki, Jun-Ichi, Tajima, Youichi, Takeda, Shin'ichi, Endo, Tamao, Kobayashi, Kazuhiro, Campbell, Kevin P., Toda, Tatsushi
Published in Human molecular genetics (15.02.2009)
Published in Human molecular genetics (15.02.2009)
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Journal Article
Comparison of the effects of agalsidase alfa and agalsidase beta on cultured human Fabry fibroblasts and Fabry mice
Sakuraba, Hitoshi, Murata-Ohsawa, Mai, Kawashima, Ikuo, Tajima, Youichi, Kotani, Masaharu, Ohshima, Toshio, Chiba, Yasunori, Takashiba, Minako, Jigami, Yoshifumi, Fukushige, Tomoko, Kanzaki, Tamotsu, Itoh, Kohji
Published in Journal of human genetics (01.03.2006)
Published in Journal of human genetics (01.03.2006)
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Journal Article
Production of Recombinant β-Hexosaminidase A, a Potential Enzyme for Replacement Therapy for Tay-Sachs and Sandhoff Diseases, in the Methylotrophic Yeast Ogataea minuta
Akeboshi, Hiromi, Chiba, Yasunori, Kasahara, Yoshiko, Takashiba, Minako, Takaoka, Yuki, Ohsawa, Mai, Tajima, Youichi, Kawashima, Ikuo, Tsuji, Daisuke, Itoh, Kohji, Sakuraba, Hitoshi, Jigami, Yoshifumi
Published in Applied and Environmental Microbiology (01.08.2007)
Published in Applied and Environmental Microbiology (01.08.2007)
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Journal Article
Structural and biochemical studies on Pompe disease and a "pseudodeficiency of acid α-glucosidase"
Tajima, Youichi, Matsuzawa, Fumiko, Aikawa, Sei-Ichi, Okumiya, Toshika, Yoshimizu, Michiru, Tsukimura, Takahiro, Ikekita, Masahiko, Tsujino, Seiichi, Tsuji, Akihiko, Edmunds, Tim, Sakuraba, Hitoshi
Published in Journal of human genetics (01.11.2007)
Published in Journal of human genetics (01.11.2007)
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Journal Article
Structural modeling of mutant α-glucosidases resulting in a processing transport defect in Pompe disease
Sugawara, Kanako, Saito, Seiji, Sekijima, Masakazu, Ohno, Kazuki, Tajima, Youichi, Kroos, Marian A, Reuser, Arnold J J, Sakuraba, Hitoshi
Published in Journal of human genetics (01.06.2009)
Published in Journal of human genetics (01.06.2009)
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Journal Article
Uptake of a Recombinant Human α-L-Iduronidase (laronidase) by Cultured Fibroblasts and Osteoblasts
Tsukimura, Takahiro, Tajima, Youichi, Kawashima, Ikuo, Fukushige, Tomoko, Kanzaki, Tamotsu, Kanekura, Takuro, Ikekita, Masahiko, Sugawara, Kanako, Suzuki, Toshihiro, Togawa, Tadayasu, Sakuraba, Hitoshi
Published in Biological & pharmaceutical bulletin (01.09.2008)
Published in Biological & pharmaceutical bulletin (01.09.2008)
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Journal Article
Establishment of immortalized Schwann cells from Fabry mice and their low uptake of recombinant α-galactosidase
Kawashima, Ikuo, Watabe, Kazuhiko, Tajima, Youichi, Fukushige, Tomoko, Kanzaki, Tamotsu, Kanekura, Takuro, Sugawara, Kanako, Ohyanagi, Naho, Suzuki, Toshihiro, Togawa, Tadayasu, Sakuraba, Hitoshi
Published in Journal of human genetics (01.12.2007)
Published in Journal of human genetics (01.12.2007)
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Journal Article
Establishment of immortalized Schwann cells from Sandhoff mice and corrective effect of recombinant human β-hexosaminidase A on the accumulated GM2 ganglioside
Ohsawa, Mai, Kotani, Masaharu, Tajima, Youichi, Tsuji, Daisuke, Ishibashi, Yasuhiro, Kuroki, Aya, Itoh, Kohji, Watabe, Kazuhiko, Sango, Kazunori, Yamanaka, Shoji, Sakuraba, Hitoshi
Published in Journal of human genetics (01.09.2005)
Published in Journal of human genetics (01.09.2005)
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Journal Article
Corrective effect on Fabry mice of yeast recombinant human alpha-galactosidase with N-linked sugar chains suitable for lysosomal delivery
Sakuraba, Hitoshi, Chiba, Yasunori, Kotani, Masaharu, Kawashima, Ikuo, Ohsawa, Mai, Tajima, Youichi, Takaoka, Yuki, Jigami, Yoshifumi, Takahashi, Hiroshi, Hirai, Yukihiko, Shimada, Takashi, Hashimoto, Yasuhiro, Ishii, Kumiko, Kobayashi, Toshihide, Watabe, Kazuhiko, Fukushige, Tomoko, Kanzaki, Tamotsu
Published in Journal of human genetics (01.04.2006)
Published in Journal of human genetics (01.04.2006)
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Journal Article
Pax6 Controls the Expression of Lewis x Epitope in the Embryonic Forebrain by Regulating α1,3-Fucosyltransferase IX Expression
Shimoda, Yasushi, Tajima, Youichi, Osanai, Taka, Katsume, Asao, Kohara, Michinori, Kudo, Takashi, Narimatsu, Hisashi, Takashima, Noriko, Ishii, Yasuo, Nakamura, Shun, Osumi, Noriko, Sanai, Yutaka
Published in The Journal of biological chemistry (18.01.2002)
Published in The Journal of biological chemistry (18.01.2002)
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Journal Article
Phospholipid storage in the myocardium of a unique Japanese case of idiopathic cardiomyopathy
Kawashima, Ikuo, Takeuchi, Ichiro, Ohsawa, Mai, Kotani, Masaharu, Tajima, Youichi, Inomata, Takayuki, Izumi, Tohru, Sakuraba, Hitoshi
Published in Clinica chimica acta (01.10.2006)
Published in Clinica chimica acta (01.10.2006)
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Journal Article
Cloning and Expression of a Novel Galactoside β1,3-Glucuronyltransferase Involved in the Biosynthesis of HNK-1 Epitope
Shimoda, Yasushi, Tajima, Youichi, Nagase, Takashi, Harii, Kiyonori, Osumi, Noriko, Sanai, Yutaka
Published in The Journal of biological chemistry (01.06.1999)
Published in The Journal of biological chemistry (01.06.1999)
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Journal Article
Identification of neuronal cell lineage-specific molecules in the neuronal differentiation of P19 EC cells and mouse central nervous system
Kotani, Masaharu, Osanai, Taka, Tajima, Youichi, Kato, Hiroko, Imada, Masato, Kaneda, Hideki, Kubo, Hideo, Sakuraba, Hitoshi
Published in Journal of neuroscience research (01.03.2002)
Published in Journal of neuroscience research (01.03.2002)
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Journal Article
Complementary DNA cloning and characterization of RANDAM-2, a type I membrane molecule specifically expressed on glutamatergic neuronal cells in the mouse cerebrum
Kotani, Masaharu, Tajima, Youichi, Osanai, Taka, Irie, Atsushi, Iwatsuki, Ken, Kanai-Azuma, Masami, Imada, Masato, Kato, Hiroko, Shitara, Hiroshi, Kubo, Hideo, Sakuraba, Hitoshi
Published in Journal of neuroscience research (01.09.2003)
Published in Journal of neuroscience research (01.09.2003)
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Journal Article