Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease
Zischka, Hans, Lichtmannegger, Josef, Schmitt, Sabine, Jägemann, Nora, Schulz, Sabine, Wartini, Daniela, Jennen, Luise, Rust, Christian, Larochette, Nathanael, Galluzzi, Lorenzo, Chajes, Veronique, Bandow, Nathan, Gilles, Valérie S, DiSpirito, Alan A, Esposito, Irene, Goettlicher, Martin, Summer, Karl H, Kroemer, Guido
Published in The Journal of clinical investigation (01.04.2011)
Published in The Journal of clinical investigation (01.04.2011)
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Journal Article
Gene expression in the liver of Long-Evans cinnamon rats during the development of hepatitis
KLEIN, Dominik, LICHTMANNEGGER, Josef, FINCKH, Matthias, SUMMER, Karl H
Published in Archives of toxicology (01.10.2003)
Published in Archives of toxicology (01.10.2003)
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Journal Article
Tracing Copper−Thiomolybdate Complexes in a Prospective Treatment for Wilson’s Disease
Zhang, Limei, Lichtmannegger, Josef, Summer, Karl H, Webb, Samuel, Pickering, Ingrid J, George, Graham N
Published in Biochemistry (Easton) (10.02.2009)
Published in Biochemistry (Easton) (10.02.2009)
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Journal Article
The biogenic methanobactin is an effective chelator for copper in a rat model for Wilson disease
Summer, Karl H., Lichtmannegger, Josef, Bandow, Nathan, Choi, Don W., DiSpirito, Alan A., Michalke, Bernhard
Published in Journal of trace elements in medicine and biology (2011)
Published in Journal of trace elements in medicine and biology (2011)
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Journal Article
Mutant rat strain lacking d-amino-acid oxidase
Konno, Ryuichi, Okamura, Tadashi, Kasai, Noriyuki, Summer, Karl H, Niwa, Akira
Published in Amino acids (01.07.2009)
Published in Amino acids (01.07.2009)
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Journal Article
Isolation of highly pure rat liver mitochondria with the aid of zone-electrophoresis in a free flow device (ZE-FFE)
Zischka, Hans, Lichtmannegger, Josef, Jägemann, Nora, Jennen, Luise, Hamöller, Daniela, Huber, Evamaria, Walch, Axel, Summer, Karl H, Göttlicher, Martin
Published in Methods in molecular biology (Clifton, N.J.) (2008)
Published in Methods in molecular biology (Clifton, N.J.) (2008)
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Journal Article
d-Amino-acid Oxidase Is Involved in d-Serine-Induced Nephrotoxicity
Maekawa, Masao, Okamura, Tadashi, Kasai, Noriyuki, Hori, Yuuichi, Summer, Karl H, Konno, Ryuichi
Published in Chemical research in toxicology (01.11.2005)
Published in Chemical research in toxicology (01.11.2005)
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Journal Article
Dissolution of copper-rich granules in hepatic lysosomes by D-penicillamine prevents the development of fulminant hepatitis in Long-Evans cinnamon rats
Klein, Dominik, Lichtmannegger, Josef, Heinzmann, Ulrich, Summer, Karl H
Published in Journal of hepatology (01.02.2000)
Published in Journal of hepatology (01.02.2000)
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Journal Article
Physiologic function of the Wilson disease gene prouct, ATP7B
Bingham, Michelle J, Teng-Jin, Ong, Summer, Karl H, Middleton, Rachel B, McArdle, Harry J
Published in The American journal of clinical nutrition (01.05.1998)
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Published in The American journal of clinical nutrition (01.05.1998)
Journal Article
Physiologic function of the Wilson disease gene product, ATP7B
Bingham, MJ, Ong, TJ, Summer, KH, Middleton, RB, McArdle, HJ
Published in The American journal of clinical nutrition (01.05.1998)
Published in The American journal of clinical nutrition (01.05.1998)
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Journal Article
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